作者
Ravi Suppiah, Joanna C Robson, Peter C Grayson, Cristina Ponte, Anthea Craven, Sara Khalid, Andrew Judge, Andrew Hutchings, Peter A Merkel, Raashid A Luqmani, Richard A Watts, DCVAS Study Group, Paul Gatenby, Catherine Hill, Dwarakanathan Ranganathan, Andreas Kronbichler, Daniel Blockmans, Lillian Barra, Simon Carette, Christian Pagnoux, Navjot Dhindsa, Aurore FifiMah, Nader Khalidi, Patrick Liang, Nataliya Milman, Christian Pineau, Xinping Tian, Guochun Wang, Tian Wang, Minghui Zhao, Vladimir Tesar, Bo Baslund, Nevin Hammam, Amira Shahin, Laura Pirila, Jukka Putaala, Bernhard Hellmich, Jörg Henes, Peter Lamprecht, Thomas Neumann, Wolfgang Schmidt, Cord Sunderkoetter, Zoltan Szekanecz, Debashish Danda, Siddharth Das, Rajiva Gupta, Liza Rajasekhar, Aman Sharma, Shrikant Wagh, Michael Clarkson, Eamonn Molloy, Carlo Salvarani, Franco Schiavon, Enrico Tombetti, Augusto Vaglio, Koichi Amano, Yoshihiro Arimura, Hiroaki Dobashi, Shouichi Fujimoto, Masayoshi Harigai, Fumio Hirano, Junichi Hirahashi, Sakae Honma, Tamihiro Kawakami, Shigeto Kobayashi, Hajime Kono, Hirofumi Makino, Kazuo Matsui, Eri Muso, Kazuo Suzuki, Kei Ikeda, Tsutomu Takeuchi, Tatsuo Tsukamoto, Shunya Uchida, Takashi Wada, Hidehiro Yamada, Kunihiro Yamagata, Wako Yumura, Kan Sow Lai, Luis Felipe FloresSuarez, Andrea Hinojosa, Bram Rutgers, PaulPeter Tak, Rebecca Grainger, Vicki Quincey, Lisa Stamp, Ravi Suppiah, Emilio Besada, Andreas Diamantopoulos, Jan Sznajd, Elsa Azevedo, Ruth Geraldes, Miguel Rodrigues, Ernestina Santos, YeongWook Song, Sergey Moiseev, Alojzija Hocˇevar, Maria Cinta Cid, Xavier Solanich Moreno, Inoshi Atukorala, Ewa Berglin, Aladdin Mohammed, Mårten Segelmark, Thomas Daikeler, Haner Direskeneli, Gulen Hatemi, Sevil Kamali, Ömer Karadag, Seval Pehlevan, Matthew Adler, Neil Basu, Iain Bruce, Kuntal Chakravarty, Bhaskar Dasgupta, Oliver Flossmann, Nagui Gendi, Alaa Hassan, Rachel Hoyles, David Jayne, Colin Jones, Rainer Klocke, Peter Lanyon, Cathy Laversuch, Raashid Luqmani, Joanna Robson, Malgorzata Magliano, Justin Mason, Win Win Maw, Iain McInnes, John Mclaren, Matthew Morgan, Ann Morgan, Chetan Mukhtyar, Edmond O'Riordan, Sanjeev Patel, Adrian Peall, Joanna Robson, Srinivasan Venkatachalam, Erin Vermaak, Ajit Menon, Richard Watts, CheeSeng Yee, Daniel Albert, Leonard Calabrese, Sharon Chung, Lindsy Forbess, Angelo Gaffo, Ora GewurzSinger, Peter Grayson, Kimberly Liang
发表日期
2022/3
期刊
Arthritis & Rheumatology
卷号
74
期号
3
页码范围
400-406
出版商
Wiley Periodicals, Inc.
简介
Objective
To develop and validate classification criteria for microscopic polyangiitis (MPA).
Methods
Patients with vasculitis or comparator diseases were recruited into an international cohort. The study proceeded in 5 phases: 1) identification of candidate items using consensus methodology, 2) prospective collection of candidate items present at the time of diagnosis, 3) datadriven reduction of the number of candidate items, 4) expert panel review of cases to define the reference diagnosis, and 5) derivation of a pointsbased risk score for disease classification in a development set using least absolute shrinkage and selection operator logistic regression, with subsequent validation of performance characteristics in an independent set of cases and comparators.
Results
The development set for MPA consisted of 149 cases of MPA and 408 comparators. The validation set consisted of an additional 142 cases of …
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