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Creutzfeld-Jakob disease (CJD) is a rare neurodegenerative disease that is clinically characterized by rapidly progressive dementia, visual disturbance, and movement disorders including myoclonus and cerebellar ataxia, both of which occur in approximately 80% of patients. 1 Over time, almost all patients enter a phase of akinetic mutism before death. Although chorea is commonly observed in variant CJD (vCJD), it is considered a rare occurrence in sporadic CJD (sCJD). 2 Here, we report a patient with sCJD with chorea as a prominent clinical feature on presentation to the hospital. A previously healthy 71-year-old woman presented with a two-month history of visual hallucinations followed by rapidly worsening cognitive function and mobility. Within six weeks of symptom onset, she became completely withdrawn and unable to recognize family members or respond to questions; her gait also progressed from …