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Among the idiopathic inflammatory myopathies (IIMs), immune-mediated necrotizing myopathies (IMNMs) have been identified as important and separate entities during the past years. A considerable wealth of studies detailing different sub-entities such as anti-signal recognition particle (SRP) and anti-HMG-CoA reductase (HMGCR)-associated myopathies has been published by different groups all over the world, and detailed knowledge about specific characteristics, pathophysiology and treatment options has accumulated. Furthermore, characteristic morphological features separating IMNM from other idiopathic inflammatory myopathies have been studied. In 2003, an expert team had defined clinicopathological criteria for IIMs during the 119th ENMC workshop, and these criteria have been widely used ever since. Fourteen years on, it was time to revisit and expand these criteria for IMNM and a team of 18 …