作者
Jo-David Fine, Robin AJ Eady, Eugene A Bauer, Johann W Bauer, Leena Bruckner-Tuderman, Adrian Heagerty, Helmut Hintner, Alain Hovnanian, Marcel F Jonkman, Irene Leigh, John A McGrath, Jemima E Mellerio, Dedee F Murrell, Hiroshi Shimizu, Jouni Uitto, Anders Vahlquist, David Woodley, Giovanna Zambruno
发表日期
2008/6/1
期刊
Journal of the American Academy of Dermatology
卷号
58
期号
6
页码范围
931-950
出版商
Mosby
简介
BACKGROUND
Since publication in 2000 of the Second International Consensus Report on Diagnosis and Classification of Epidermolysis Bullosa, many advances have been made to our understanding of this group of diseases, both clinically and molecularly. At the same time, new epidermolysis bullosa (EB) subtypes have been described and similarities with some other diseases have been identified.
OBJECTIVE
We sought to arrive at a new consensus of the classification of EB subtypes.
RESULTS
We now present a revised classification system that takes into account the new advances, as well as encompassing other inherited diseases that should also be included within the EB spectrum, based on the presence of blistering and mechanical fragility. Current recommendations are made on the use of specific diagnostic tests, with updates on the findings known to occur within each of the major EB subtypes …
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JD Fine, RAJ Eady, EA Bauer, JW Bauer… - Journal of the American Academy of Dermatology, 2008