Assembly of mitochondrial cytochrome c-oxidase, a complicated and highly regulated cellular process F Fontanesi, IC Soto, D Horn, A Barrientos American Journal of Physiology-Cell Physiology 291 (6), C1129-C1147, 2006 | 316 | 2006 |
Mitochondrial complex I plays an essential role in human respirasome assembly D Moreno-Lastres, F Fontanesi, I García-Consuegra, MA Martín, J Arenas, ... Cell metabolism 15 (3), 324-335, 2012 | 308 | 2012 |
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using polarography and spectrophotometric enzyme assays A Barrientos, F Fontanesi, F Díaz Current protocols in human genetics 63 (1), 19.3. 1-19.3. 14, 2009 | 286 | 2009 |
Biogenesis and assembly of eukaryotic cytochrome c oxidase catalytic core IC Soto, F Fontanesi, J Liu, A Barrientos Biochimica Et Biophysica Acta (BBA)-Bioenergetics 1817 (6), 883-897, 2012 | 266 | 2012 |
Mutations in SLC25A46, encoding a UGO1-like protein, cause an optic atrophy spectrum disorder AJ Abrams, RB Hufnagel, A Rebelo, C Zanna, N Patel, MA Gonzalez, ... Nature genetics 47 (8), 926-932, 2015 | 214 | 2015 |
Cytochrome c oxidase biogenesis: New levels of regulation F Fontanesi, IC Soto, A Barrientos IUBMB life 60 (9), 557-568, 2008 | 206 | 2008 |
Complete loss-of-function of the heart/muscle-specific adenine nucleotide translocator is associated with mitochondrial myopathy and cardiomyopathy L Palmieri, S Alberio, I Pisano, T Lodi, M Meznaric-Petrusa, J Zidar, ... Human molecular genetics 14 (20), 3079-3088, 2005 | 203 | 2005 |
Mitochondrial ribosome assembly in health and disease D De Silva, YT Tu, A Amunts, F Fontanesi, A Barrientos Cell Cycle 14 (14), 2226-2250, 2015 | 199 | 2015 |
ATP-binding cassette A1 deficiency causes cardiolipin-driven mitochondrial dysfunction in podocytes GM Ducasa, A Mitrofanova, SK Mallela, X Liu, J Molina, A Sloan, ... The Journal of clinical investigation 129 (8), 3387-3400, 2019 | 135 | 2019 |
Suppression mechanisms of COX assembly defects in yeast and human: insights into the COX assembly process A Barrientos, K Gouget, D Horn, IC Soto, F Fontanesi Biochimica et Biophysica Acta (BBA)-Molecular Cell Research 1793 (1), 97-107, 2009 | 126 | 2009 |
COX7A2L is a mitochondrial complex III binding protein that stabilizes the III2+ IV supercomplex without affecting respirasome formation R Pérez-Pérez, T Lobo-Jarne, D Milenkovic, A Mourier, A Bratic, ... Cell reports 16 (9), 2387-2398, 2016 | 116 | 2016 |
Respiratory supercomplexes enhance electron transport by decreasing cytochrome c diffusion distance J Berndtsson, A Kohler, S Rathore, L Marin‐Buera, H Dawitz, J Diessl, ... EMBO reports 21 (12), e51015, 2020 | 97 | 2020 |
Cox25 teams up with Mss51, Ssc1, and Cox14 to regulate mitochondrial cytochrome c oxidase subunit 1 expression and assembly in Saccharomyces cerevisiae F Fontanesi, P Clemente, A Barrientos Journal of Biological Chemistry 286 (1), 555-566, 2011 | 95 | 2011 |
Mss51 and Ssc1 Facilitate Translational Regulation of Cytochrome c Oxidase Biogenesis F Fontanesi, IC Soto, D Horn, A Barrientos Molecular and cellular biology 30 (1), 245-259, 2010 | 93 | 2010 |
Mutations in AAC2, equivalent to human adPEO-associated ANT1 mutations, lead to defective oxidative phosphorylation in Saccharomyces cerevisiae and affect … F Fontanesi, L Palmieri, P Scarcia, T Lodi, C Donnini, A Limongelli, ... Human Molecular Genetics 13 (9), 923-934, 2004 | 91 | 2004 |
A heme-sensing mechanism in the translational regulation of mitochondrial cytochrome c oxidase biogenesis IC Soto, F Fontanesi, RS Myers, P Hamel, A Barrientos Cell metabolism 16 (6), 801-813, 2012 | 81 | 2012 |
Redox and Reactive Oxygen Species Regulation of Mitochondrial Cytochrome c Oxidase Biogenesis M Bourens, F Fontanesi, IC Soto, J Liu, A Barrientos Antioxidants & redox signaling 19 (16), 1940-1952, 2013 | 77 | 2013 |
Multiple pathways coordinate assembly of human mitochondrial complex IV and stabilization of respiratory supercomplexes T Lobo‐Jarne, R Pérez‐Pérez, F Fontanesi, A Timón‐Gómez, I Wittig, ... The EMBO journal 39 (14), e103912, 2020 | 70 | 2020 |
Evaluation of the mitochondrial respiratory chain and oxidative phosphorylation system using blue native gel electrophoresis F Díaz, A Barrientos, F Fontanesi Current protocols in human genetics 63 (1), 19.4. 1-19.4. 12, 2009 | 68 | 2009 |
Aberrant Translation of Cytochrome c Oxidase Subunit 1 mRNA Species in the Absence of Mss51p in the Yeast Saccharomyces cerevisiae A Zambrano, F Fontanesi, A Solans, RL de Oliveira, TD Fox, A Tzagoloff, ... Molecular biology of the cell 18 (2), 523-535, 2007 | 66 | 2007 |