Sporadic and familial CJD: classification and characterisation P Gambetti, Q Kong, W Zou, P Parchi, SG Chen British medical bulletin 66 (1), 213-239, 2003 | 690 | 2003 |
A novel human disease with abnormal prion protein sensitive to protease P Gambetti, Z Dong, J Yuan, X Xiao, M Zheng, A Alshekhlee, R Castellani, ... Annals of Neurology: Official Journal of the American Neurological …, 2008 | 364 | 2008 |
Chronic wasting disease of elk: transmissibility to humans examined by transgenic mouse models Q Kong, S Huang, W Zou, D Vanegas, M Wang, D Wu, J Yuan, M Zheng, ... Journal of Neuroscience 25 (35), 7944-7949, 2005 | 321 | 2005 |
Mammalian prions generated from bacterially expressed prion protein in the absence of any mammalian cofactors JI Kim, I Cali, K Surewicz, Q Kong, GJ Raymond, R Atarashi, B Race, ... Journal of Biological Chemistry 285 (19), 14083-14087, 2010 | 269 | 2010 |
Variably protease‐sensitive prionopathy: a new sporadic disease of the prion protein WQ Zou, G Puoti, X Xiao, J Yuan, L Qing, I Cali, M Shimoji, ... Annals of neurology 68 (2), 162-172, 2010 | 265 | 2010 |
Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain Q Kong, M Zheng, C Casalone, L Qing, S Huang, B Chakraborty, P Wang, ... Journal of virology 82 (7), 3697-3701, 2008 | 189 | 2008 |
Inherited prion diseases Q Kong, WK Surewicz, RB Petersen, W Zou, SG Chen, P Gambetti, ... Prion biology and diseases, 673-776, 2004 | 175 | 2004 |
Insoluble aggregates and protease-resistant conformers of prion protein in uninfected human brains J Yuan, X Xiao, J McGeehan, Z Dong, I Cali, H Fujioka, Q Kong, G Kneale, ... Journal of Biological Chemistry 281 (46), 34848-34858, 2006 | 134 | 2006 |
Prion seeding activity and infectivity in skin samples from patients with sporadic Creutzfeldt-Jakob disease CD Orrú, J Yuan, BS Appleby, B Li, Y Li, D Winner, Z Wang, YA Zhan, ... Science translational medicine 9 (417), eaam7785, 2017 | 132 | 2017 |
Molecular biology and pathology of prion strains in sporadic human prion diseases P Gambetti, I Cali, S Notari, Q Kong, WQ Zou, WK Surewicz Acta neuropathologica 121, 79-90, 2011 | 123 | 2011 |
Abnormal brain iron homeostasis in human and animal prion disorders A Singh, AO Isaac, X Luo, ML Mohan, ML Cohen, F Chen, Q Kong, J Bartz, ... PLoS pathogens 5 (3), e1000336, 2009 | 113 | 2009 |
Prion protein (PrP) knock-out mice show altered iron metabolism: a functional role for PrP in iron uptake and transport A Singh, Q Kong, X Luo, RB Petersen, H Meyerson, N Singh PLoS One 4 (7), e6115, 2009 | 111 | 2009 |
Open reading frames of turnip crinkle virus involved in satellite symptom expression and incompatibility with Arabidopsis thaliana ecotype Dijon JW Oh, Q Kong, C Song, CD Carpenter, AE Simon MPMI-Molecular Plant Microbe Interactions 8 (6), 979-987, 1995 | 95 | 1995 |
DNA breaks in hypermutating immunoglobulin genes: evidence for a break-and-repair pathway of somatic hypermutation Q Kong, N Maizels Genetics 158 (1), 369-378, 2001 | 92 | 2001 |
Amyloid fibrils from the N-terminal prion protein fragment are infectious JK Choi, I Cali, K Surewicz, Q Kong, P Gambetti, WK Surewicz Proceedings of the National Academy of Sciences 113 (48), 13851-13856, 2016 | 91 | 2016 |
Human prion protein sequence elements impede cross-species chronic wasting disease transmission TD Kurt, L Jiang, N Fernández-Borges, C Bett, J Liu, T Yang, TR Spraker, ... The Journal of clinical investigation 125 (4), 1485-1496, 2015 | 89 | 2015 |
Small Protease Sensitive Oligomers of PrPSc in Distinct Human Prions Determine Conversion Rate of PrPC C Kim, T Haldiman, K Surewicz, Y Cohen, W Chen, J Blevins, MS Sy, ... Public Library of Science 8 (8), e1002835, 2012 | 88 | 2012 |
α-Cleavage of cellular prion protein J Liang, Q Kong Prion 6 (5), 453-460, 2012 | 84 | 2012 |
Prion disease tempo determined by host-dependent substrate reduction CE Mays, C Kim, T Haldiman, J van der Merwe, A Lau, J Yang, J Grams, ... The Journal of clinical investigation 124 (2), 2014 | 81 | 2014 |
Somatic hypermutation and the three R's: repair, replication and recombination RS Harris, Q Kong, N Maizels Mutation Research/Reviews in Mutation Research 436 (2), 157-178, 1999 | 81 | 1999 |