Sideroflexin 4 is a complex I assembly factor that interacts with the MCIA complex and is required for the assembly of the ND2 module TD Jackson, JJ Crameri, L Muellner-Wong, AE Frazier, CS Palmer, ... Proceedings of the National Academy of Sciences 119 (13), e2115566119, 2022 | 19 | 2022 |
Mitochondrial biology and dysfunction in secondary mitochondrial disease MJ Baker, JJ Crameri, DR Thorburn, AE Frazier, D Stojanovski Open Biology 12 (12), 220274, 2022 | 12 | 2022 |
Human Tim8a, Tim8b and Tim13 are auxiliary assembly factors of mature Complex IV AJ Anderson, JJ Crameri, CS Ang, TR Malcolm, Y Kang, MJ Baker, ... EMBO reports 24 (8), e56430, 2023 | 9 | 2023 |
Loss of mitochondrial fatty acid β‐oxidation protein short‐chain Enoyl‐CoA hydratase disrupts oxidative phosphorylation protein complex stability and function H Burgin, AJ Sharpe, S Nie, M Ziemann, JJ Crameri, D Stojanovski, J Pitt, ... The FEBS Journal 290 (1), 225-246, 2023 | 8 | 2023 |
CLPB disaggregase dysfunction impacts the functional integrity of the proteolytic SPY complex MJ Baker, KU Blau, AJ Anderson, CS Palmer, LF Fielden, JJ Crameri, ... Journal of Cell Biology 223 (3), e202305087, 2024 | 2 | 2024 |
Stimulating mitochondrial Biogenesis with deoxyribonucleosides increases functional capacity in ECHS1-Deficient cells HJ Burgin, JJ Crameri, D Stojanovski, MIGL Sanchez, M Ziemann, ... International Journal of Molecular Sciences 23 (20), 12610, 2022 | 1 | 2022 |
Monitoring the in vitro import and assembly of mitochondrial precursor proteins into mammalian mitochondria JJ Crameri, D Stojanovski Academic Press, 2024 | | 2024 |
Reduced Protein Import via TIM23 SORT Drives Disease Pathology in TIMM50-Associated Mitochondrial Disease JJ Crameri, CS Palmer, T Stait, TD Jackson, M Lynch, A Sinclair, ... Molecular and Cellular Biology, 1-19, 2024 | | 2024 |