关注
Vincent Paupe
Vincent Paupe
未知所在单位机构
在 cam.ac.uk 的电子邮件经过验证
标题
引用次数
引用次数
年份
Mitochondrial dynamics: overview of molecular mechanisms
L Tilokani, S Nagashima, V Paupe, J Prudent
Essays in biochemistry 62 (3), 341-360, 2018
11412018
The mitochondrial RNA-binding protein GRSF1 localizes to RNA granules and is required for posttranscriptional mitochondrial gene expression
H Antonicka, F Sasarman, T Nishimura, V Paupe, EA Shoubridge
Cell metabolism 17 (3), 386-398, 2013
2372013
Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia
V Paupe, EP Dassa, S Goncalves, F Auchère, M Lönn, A Holmgren, ...
PloS one 4 (1), e4253, 2009
2322009
SLC25A46 is required for mitochondrial lipid homeostasis and cristae maintenance and is responsible for Leigh syndrome
A Janer, J Prudent, V Paupe, S Fahiminiya, J Majewski, N Sgarioto, ...
EMBO molecular medicine 8 (9), 1019-1038, 2016
1762016
Golgi-derived PI(4)P-containing vesicles drive late steps of mitochondrial division
S Nagashima, LC Tábara, L Tilokani, V Paupe, H Anand, JH Pogson, ...
Science 367 (6484), 1366-1371, 2020
1722020
CCDC90A (MCUR1) is a cytochrome c oxidase assembly factor and not a regulator of the mitochondrial calcium uniporter
V Paupe, J Prudent, EP Dassa, OZ Rendon, EA Shoubridge
Cell metabolism 21 (1), 109-116, 2015
1512015
New insights into the role of mitochondrial calcium homeostasis in cell migration
V Paupe, J Prudent
Biochemical and biophysical research communications 500 (1), 75-86, 2018
1362018
Expression of the alternative oxidase complements cytochrome c oxidase deficiency in human cells
EP Dassa, E Dufour, S Gonçalves, V Paupe, GAJ Hakkaart, HT Jacobs, ...
EMBO molecular medicine 1 (1), 30-36, 2009
1092009
Fumarate induces vesicular release of mtDNA to drive innate immunity
V Zecchini, V Paupe, I Herranz-Montoya, J Janssen, IMN Wortel, JL Morris, ...
Nature 615 (7952), 499-506, 2023
1062023
Deferiprone targets aconitase: implication for Friedreich's ataxia treatment
S Goncalves, V Paupe, EP Dassa, P Rustin
BMC neurology 8, 1-4, 2008
792008
Mitochondrial translation is required for sustained killing by cytotoxic T cells
M Lisci, PR Barton, LO Randzavola, CY Ma, JM Marchingo, DA Cantrell, ...
Science 374 (6565), eabe9977, 2021
662021
The gene responsible for Dyggve-Melchior-Clausen syndrome encodes a novel peripheral membrane protein dynamically associated with the Golgi apparatus
A Dimitrov, V Paupe, C Gueudry, JB Sibarita, G Raposo, O Vielemeyer, ...
Human Molecular Genetics 18 (3), 440-453, 2009
662009
Recent advances in Dyggve–Melchior–Clausen syndrome
V Paupe, T Gilbert, M Le Merrer, A Munnich, V Cormier-Daire, ...
Molecular genetics and metabolism 83 (1-2), 51-59, 2004
532004
Rapid determination of tricarboxylic acid cycle enzyme activities in biological samples
S Goncalves, V Paupe, EP Dassa, JJ Brière, J Favier, ...
BMC biochemistry 11, 1-8, 2010
392010
Dyggve–Melchior–Clausen syndrome and Smith–McCort dysplasia: clinical and molecular findings in three families supporting genetic heterogeneity in Smith–McCort dysplasia
LM Neumann, VE Ghouzzi, V Paupe, HP Weber, E Fastnacht, A Leenen, ...
American Journal of Medical Genetics Part A 140 (5), 421-426, 2006
312006
AMPK-dependent phosphorylation of MTFR1L regulates mitochondrial morphology
L Tilokani, FM Russell, S Hamilton, DM Virga, M Segawa, V Paupe, ...
Science advances 8 (45), eabo7956, 2022
252022
The mtDNA NARP mutation activates the actin-Nrf2 signaling of antioxidant defenses
EP Dassa, V Paupe, S Gonçalves, P Rustin
Biochemical and biophysical research communications 368 (3), 620-624, 2008
122008
Genome-wide CRISPR/Cas9 screen shows that loss of GET4 increases mitochondria-endoplasmic reticulum contact sites and is neuroprotective
EL Wilson, Y Yu, NS Leal, JA Woodward, N Patikas, JL Morris, SF Field, ...
Cell Death & Disease 15 (3), 203, 2024
32024
Expression pattern of the gene responsible for Dyggve-Melchlor-Clausen syndrome (Dym) during human development.
V El Ghouzzi, G Mattei, V Paupe, T Atie-Bitach, A Munnich, M Vekemans, ...
AMERICAN JOURNAL OF HUMAN GENETICS 73 (5), 321-321, 2003
12003
MTFP1 controls mitochondrial fusion to regulate inner membrane quality control and maintain mtDNA levels
LC Tábara, SP Burr, M Frison, SR Chowdhury, V Paupe, Y Nie, ...
Cell, 2024
2024
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