Mitochondrial dynamics: overview of molecular mechanisms L Tilokani, S Nagashima, V Paupe, J Prudent Essays in biochemistry 62 (3), 341-360, 2018 | 1141 | 2018 |
The mitochondrial RNA-binding protein GRSF1 localizes to RNA granules and is required for posttranscriptional mitochondrial gene expression H Antonicka, F Sasarman, T Nishimura, V Paupe, EA Shoubridge Cell metabolism 17 (3), 386-398, 2013 | 237 | 2013 |
Impaired nuclear Nrf2 translocation undermines the oxidative stress response in Friedreich ataxia V Paupe, EP Dassa, S Goncalves, F Auchère, M Lönn, A Holmgren, ... PloS one 4 (1), e4253, 2009 | 232 | 2009 |
SLC25A46 is required for mitochondrial lipid homeostasis and cristae maintenance and is responsible for Leigh syndrome A Janer, J Prudent, V Paupe, S Fahiminiya, J Majewski, N Sgarioto, ... EMBO molecular medicine 8 (9), 1019-1038, 2016 | 176 | 2016 |
Golgi-derived PI(4)P-containing vesicles drive late steps of mitochondrial division S Nagashima, LC Tábara, L Tilokani, V Paupe, H Anand, JH Pogson, ... Science 367 (6484), 1366-1371, 2020 | 172 | 2020 |
CCDC90A (MCUR1) is a cytochrome c oxidase assembly factor and not a regulator of the mitochondrial calcium uniporter V Paupe, J Prudent, EP Dassa, OZ Rendon, EA Shoubridge Cell metabolism 21 (1), 109-116, 2015 | 151 | 2015 |
New insights into the role of mitochondrial calcium homeostasis in cell migration V Paupe, J Prudent Biochemical and biophysical research communications 500 (1), 75-86, 2018 | 136 | 2018 |
Expression of the alternative oxidase complements cytochrome c oxidase deficiency in human cells EP Dassa, E Dufour, S Gonçalves, V Paupe, GAJ Hakkaart, HT Jacobs, ... EMBO molecular medicine 1 (1), 30-36, 2009 | 109 | 2009 |
Fumarate induces vesicular release of mtDNA to drive innate immunity V Zecchini, V Paupe, I Herranz-Montoya, J Janssen, IMN Wortel, JL Morris, ... Nature 615 (7952), 499-506, 2023 | 106 | 2023 |
Deferiprone targets aconitase: implication for Friedreich's ataxia treatment S Goncalves, V Paupe, EP Dassa, P Rustin BMC neurology 8, 1-4, 2008 | 79 | 2008 |
Mitochondrial translation is required for sustained killing by cytotoxic T cells M Lisci, PR Barton, LO Randzavola, CY Ma, JM Marchingo, DA Cantrell, ... Science 374 (6565), eabe9977, 2021 | 66 | 2021 |
The gene responsible for Dyggve-Melchior-Clausen syndrome encodes a novel peripheral membrane protein dynamically associated with the Golgi apparatus A Dimitrov, V Paupe, C Gueudry, JB Sibarita, G Raposo, O Vielemeyer, ... Human Molecular Genetics 18 (3), 440-453, 2009 | 66 | 2009 |
Recent advances in Dyggve–Melchior–Clausen syndrome V Paupe, T Gilbert, M Le Merrer, A Munnich, V Cormier-Daire, ... Molecular genetics and metabolism 83 (1-2), 51-59, 2004 | 53 | 2004 |
Rapid determination of tricarboxylic acid cycle enzyme activities in biological samples S Goncalves, V Paupe, EP Dassa, JJ Brière, J Favier, ... BMC biochemistry 11, 1-8, 2010 | 39 | 2010 |
Dyggve–Melchior–Clausen syndrome and Smith–McCort dysplasia: clinical and molecular findings in three families supporting genetic heterogeneity in Smith–McCort dysplasia LM Neumann, VE Ghouzzi, V Paupe, HP Weber, E Fastnacht, A Leenen, ... American Journal of Medical Genetics Part A 140 (5), 421-426, 2006 | 31 | 2006 |
AMPK-dependent phosphorylation of MTFR1L regulates mitochondrial morphology L Tilokani, FM Russell, S Hamilton, DM Virga, M Segawa, V Paupe, ... Science advances 8 (45), eabo7956, 2022 | 25 | 2022 |
The mtDNA NARP mutation activates the actin-Nrf2 signaling of antioxidant defenses EP Dassa, V Paupe, S Gonçalves, P Rustin Biochemical and biophysical research communications 368 (3), 620-624, 2008 | 12 | 2008 |
Genome-wide CRISPR/Cas9 screen shows that loss of GET4 increases mitochondria-endoplasmic reticulum contact sites and is neuroprotective EL Wilson, Y Yu, NS Leal, JA Woodward, N Patikas, JL Morris, SF Field, ... Cell Death & Disease 15 (3), 203, 2024 | 3 | 2024 |
Expression pattern of the gene responsible for Dyggve-Melchlor-Clausen syndrome (Dym) during human development. V El Ghouzzi, G Mattei, V Paupe, T Atie-Bitach, A Munnich, M Vekemans, ... AMERICAN JOURNAL OF HUMAN GENETICS 73 (5), 321-321, 2003 | 1 | 2003 |
MTFP1 controls mitochondrial fusion to regulate inner membrane quality control and maintain mtDNA levels LC Tábara, SP Burr, M Frison, SR Chowdhury, V Paupe, Y Nie, ... Cell, 2024 | | 2024 |