| Chaperones in control of protein disaggregation K Liberek, A Lewandowska, S Ziętkiewicz The EMBO journal 27 (2), 328-335, 2008 | 533 | 2008 |
| Successive and synergistic action of the Hsp70 and Hsp100 chaperones in protein disaggregation K Ziȩtkiewicz, Szymon, Krzewska, Joanna, Liberek Journal of Biological Chemistry 279 (43), 44376-44383, 2004 | 185 | 2004 |
| Hsp70 displaces small heat shock proteins from aggregates to initiate protein refolding S Żwirowski, A Kłosowska, I Obuchowski, NB Nillegoda, A Piróg, ... The EMBO journal 36 (6), 783-796, 2017 | 157 | 2017 |
| CLPB mutations cause 3-methylglutaconic aciduria, progressive brain atrophy, intellectual disability, congenital neutropenia, cataracts, movement disorder SB Wortmann, S Ziętkiewicz, M Kousi, R Szklarczyk, TB Haack, ... The American Journal of Human Genetics 96 (2), 245-257, 2015 | 129 | 2015 |
| Distinct activities of Escherichia coli small heat shock proteins IbpA and IbpB promote efficient protein disaggregation E Ratajczak, S Ziętkiewicz, K Liberek Journal of molecular biology 386 (1), 178-189, 2009 | 128 | 2009 |
| Hsp70 chaperone machine remodels protein aggregates at the initial step of Hsp70-Hsp100-dependent disaggregation S Ziętkiewicz, A Lewandowska, P Stocki, K Liberek Journal of Biological Chemistry 281 (11), 7022-7029, 2006 | 117 | 2006 |
| Disruption of ionic interactions between the nucleotide binding domain 1 (NBD1) and middle (M) domain in Hsp100 disaggregase unleashes toxic hyperactivity and partial … N Lipińska, S Ziętkiewicz, A Sobczak, A Jurczyk, W Potocki, E Morawiec, ... Journal of Biological Chemistry 288 (4), 2857-2869, 2013 | 73 | 2013 |
| Importance of N-and C-terminal regions of IbpA, Escherichia coli small heat shock protein, for chaperone function and oligomerization J Stróżecka, E Chruściel, E Górna, A Szymańska, S Ziętkiewicz, K Liberek Journal of Biological Chemistry 287 (4), 2843-2853, 2012 | 51 | 2012 |
| IbpA the small heat shock protein from Escherichia coli forms fibrils in the absence of its cochaperone IbpB E Ratajczak, J Stróżecka, M Matuszewska, S Ziętkiewicz, ... FEBS letters 584 (11), 2253-2257, 2010 | 36 | 2010 |
| Low renal but high extrarenal phenotype variability in Schimke immuno-osseous dysplasia BS Lipska-Ziętkiewicz, J Gellermann, O Boyer, O Gribouval, S Ziętkiewicz, ... PloS one 12 (8), e0180926, 2017 | 35 | 2017 |
| Neutropenia and intellectual disability are hallmarks of biallelic and de novo CLPB deficiency SB Wortmann, S Ziętkiewicz, S Guerrero-Castillo, RG Feichtinger, ... Genetics in Medicine 23 (9), 1705-1714, 2021 | 24 | 2021 |
| Variation of the clinical spectrum and genotype-phenotype associations in Coenzyme Q10 deficiency associated glomerulopathy. S Drovandi, BS Lipska-Ziętkiewicz, F Ozaltin, F Emma, B Gulhan, O Boyer, ... Kidney International, 2022 | 23 | 2022 |
| CLPB (caseinolytic peptidase B homolog), the first mitochondrial protein refoldase associated with human disease D Mróz, H Wyszkowski, T Szablewski, K Zawieracz, R Dutkiewicz, K Bury, ... Biochimica Et Biophysica Acta (BBA)-General Subjects 1864 (4), 129512, 2020 | 22 | 2020 |
| c. 1810C> T Polymorphism of NTRK1 Gene is associated with reduced Survival in Neuroblastoma Patients BS Lipska, E Drożynska, P Scaruffi, GP Tonini, E Iżycka-Świeszewska, ... BMC cancer 9 (1), 1-9, 2009 | 21 | 2009 |
| Conformational stability of the full‐atom hexameric model of the ClpB chaperone from Escherichia coli S Ziętkiewicz, MJ Ślusarz, R Ślusarz, K Liberek, S Rodziewicz‐Motowidło Biopolymers 93 (1), 47-60, 2010 | 16 | 2010 |
| Syndromic chorioretinal coloboma associated with heterozygous de novo RARA mutation affecting an amino acid critical for retinoic acid interaction A Jakubiuk‐Tomaszuk, V Murcia Pienkowski, S Zietkiewicz, M Rydzanicz, ... Clinical genetics 96 (4), 371-375, 2019 | 8 | 2019 |
| Whole exome sequencing identifies a homozygous POLG2 missense variant in an adult patient presenting with optic atrophy, movement disorders, premature ovarian failure and … P Dosekova, A Dubiel, A Karlowicz, S Zietkiewicz, M Rydzanicz, ... European journal of medical genetics 63 (4), 103821, 2020 | 7 | 2020 |
| Dispose to the pole—protein aggregation control in bacteria S Ziętkiewicz, K Liberek The EMBO journal 29 (5), 869-870, 2010 | 4 | 2010 |
| Expression, purification, and efficient refolding of the extracellular domain of Escherichia coli-expressed signaling receptor herpesvirus entry mediator M Szymczak, S Ziętkiewicz, K Kuncewicz, S Rodziewicz-Motowidło, ... Protein expression and purification 164, 105450, 2019 | 3 | 2019 |
| Case Report: Lennox–Gastaut Epileptic Encephalopathy Responsive to Cannabidiol Treatment Associated With a Novel de novo Mosaic SHANK1 Variant J Paprocka, S Ziętkiewicz, J Kosińska, E Kaczorowska, R Płoski Frontiers in Genetics 12, 735292, 2021 | 1 | 2021 |
