The ubiquitin ligase UBR5 suppresses proteostasis collapse in pluripotent stem cells from Huntington’s disease patients S Koyuncu, I Saez, HJ Lee, R Gutierrez-Garcia, W Pokrzywa, A Fatima, ... Nature communications 9 (1), 2886, 2018 | 97 | 2018 |
Somatic increase of CCT8 mimics proteostasis of human pluripotent stem cells and extends C. elegans lifespan A Noormohammadi, A Khodakarami, R Gutierrez-Garcia, HJ Lee, ... Nature communications 7 (1), 13649, 2016 | 87 | 2016 |
Proteostasis of huntingtin in health and disease S Koyuncu, A Fatima, R Gutierrez-Garcia, D Vilchez International journal of molecular sciences 18 (7), 1568, 2017 | 60 | 2017 |
Mechanisms of protein homeostasis (proteostasis) maintain stem cell identity in mammalian pluripotent stem cells A Noormohammadi, G Calculli, R Gutierrez-Garcia, A Khodakarami, ... Cellular and Molecular Life Sciences 75, 275-290, 2018 | 52 | 2018 |
Insights into the ubiquitin-proteasome system of human embryonic stem cells I Saez, S Koyuncu, R Gutierrez-Garcia, C Dieterich, D Vilchez Scientific reports 8 (1), 4092, 2018 | 50 | 2018 |
Embryonic stem cells: a novel paradigm to study proteostasis? HJ Lee, R Gutierrez‐Garcia, D Vilchez The FEBS journal 284 (3), 391-398, 2017 | 40 | 2017 |
Mechanism suppressing H3K9 trimethylation in pluripotent stem cells and its demise by polyQ-expanded huntingtin mutations D Irmak, A Fatima, R Gutiérrez-Garcia, MM Rinschen, P Wagle, J Altmüller, ... Human Molecular Genetics 27 (23), 4117-4134, 2018 | 26 | 2018 |
Adaptive responses of mitochondria to mild copper deprivation involve changes in morphology, OXPHOS remodeling and bioenergetics LM Ruiz, EL Jensen, RI Bustos, G Argüelloa, R Gutierrez‐Garcia, ... Journal of Cellular Physiology 229 (5), 607-619, 2014 | 24 | 2014 |
Induced pluripotent stem cells from Huntington’s disease patients: a promising approach to define and correct disease-related alterations A Fatima, R Gutiérrez-Garcia, D Vilchez Neural regeneration research 14 (5), 769-770, 2019 | 13 | 2019 |
Identification and molecular characterization of five putative toxins from the venom gland of the snake Philodryas chamissonis (Serpentes: Dipsadidae) FA Urra, R Pulgar, R Gutiérrez, C Hodar, V Cambiazo, A Labra Toxicon 108, 19-31, 2015 | 12 | 2015 |
Physiological copper exposure in Jurkat cells induces changes in the expression of genes encoding cholesterol biosynthesis proteins R Gutiérrez-García, T del Pozo, M Suazo, V Cambiazo, M González BioMetals, 1-8, 2013 | 11 | 2013 |
G3BP1-dependent mechanism suppressing protein aggregation in Huntington’s models and its demise upon stress granule assembly R Gutiérrez-Garcia, S Koyuncu, F Hommen, S Bilican, HJ Lee, A Fatima, ... Human molecular genetics 32 (10), 1607-1621, 2023 | 10 | 2023 |
Comparative transcriptome profiling in a segregating peach population with contrasting juiciness phenotypes T Del Pozo, S Miranda, M Latorre, F Olivares, L Pavez, R Gutiérrez, ... Journal of agricultural and food chemistry 67 (5), 1598-1607, 2019 | 7 | 2019 |
In planta expression of human polyQ-expanded huntingtin fragment reveals mechanisms to prevent disease-related protein aggregation E Llamas, S Koyuncu, HJ Lee, M Wehrmann, R Gutierrez-Garcia, ... Nature aging 3 (11), 1345-1357, 2023 | 5 | 2023 |
Identification of reference genes for quantitative real-time PCR studies in human cell lines under copper and zinc exposure T Del Pozo, R Gutiérrez-Garcia, M Latorre, M González, M Suazo Biometals 29, 935-944, 2016 | 5 | 2016 |
CCS mRNA transcripts and serum CCS protein as copper marker in adults suffering inflammatory processes M Araya, R Gutiérrez, M Arredondo Biometals 27, 645-652, 2014 | 5 | 2014 |
Chloroplast protein import determines plant proteostasis and retrograde signaling E Llamas, S Koyuncu, HJ Lee, R Gutierrez-Garcia, N Dunken, N Charura, ... BioRxiv, 2022.03. 19.484971, 2022 | 4 | 2022 |
Author Correction: The ubiquitin ligase UBR5 suppresses proteostasis collapse in pluripotent stem cells from Huntington’s disease patients S Koyuncu, I Saez, HJ Lee, R Gutierrez-Garcia, W Pokrzywa, A Fatima, ... Nature Communications 11, 2020 | 1 | 2020 |
The ubiquitin ligase UBR5 suppresses proteostasis collapse in pluripotent stem cells from Huntington's disease patients (vol 9, 2886, 2018) S Koyuncu, I Saez, HJ Lee, R Gutierrez-Garcia, W Pokrzywa, A Fatima, ... NATURE COMMUNICATIONS 11 (1), 2020 | | 2020 |
来自亨廷顿病患者的诱导多能干细胞: 定义和纠正疾病相关改变的有希望的方法 A Fatima, R Gutiérrez-Garcia, D Vilchez 中国神经再生研究 (英文版) 14 (5), 769, 2019 | | 2019 |