Ventricular tachycardia in Ebstein's anomaly patients is rare and increases the risk of
sudden death up to 6 times. We present two cases of Ebstein's anomaly, the first of them with
a history of Glenn surgery and biological prosthesis at tricuspid position and the second
case without surgical repair. Both admitted to the emergency room due to ventricular
tachycardia poorly tolerated. Detailed substrate characterization and pace mapping showed
fragmented signals in the area of atrialized right ventricle and correlated were pace mapping …