Background Myotonic dystrophy type 1 (MD1) is a neuromuscular disorder with potential
involvement of the heart and increased risk of sudden death. Considering the importance of …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Background—Myotonic dystrophy type 2 (DM2) is a genetic disorder characterized by
skeletal muscle symptoms, metabolic changes, and cardiac involvement. Histopathologic …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

Objective Cardiac disease accounts for a large burden of premature mortality and morbidity
in patients with type 1 myotonic dystrophy (MD). However, little is known about structural …

In myotonic dystrophy type 2 (DM2/PROMM), cardiac muscle involvement is usually more
benign than in DM1, but clinically severe cardiomyopathy has been reported in some …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

Background Myotonic dystrophy type 1 (DM1) is associated with increased cardiac morbidity
and mortality. Therefore, assessment of cardiac involvement and risk stratification for sudden …

Myotonic dystrophy (DM) is an inherited disorder transmitted in an autosomal dominant
fashion and characterized by myotonia with dystrophic involvement of muscles and other …

Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …