Variation in cilia protein genes and progression of lung disease in cystic fibrosis

E Blue, TL Louie, JX Chong, SJ Hebbring… - Annals of the …, 2018 - atsjournals.org
Rationale: Cystic fibrosis, like primary ciliary dyskinesia, is an autosomal recessive disorder
characterized by abnormal mucociliary clearance and obstructive lung disease. We …

[HTML][HTML] Variation in Cilia Protein Genes and Progression of Lung Disease in Cystic Fibrosis

E Blue, TL Louie, JX Chong, SJ Hebbring… - Annals of the …, 2018 - ncbi.nlm.nih.gov
Rationale: Cystic fibrosis, like primary ciliary dyskinesia, is an autosomal recessive disorder
characterized by abnormal mucociliary clearance and obstructive lung disease. We …

Variation in Cilia Protein Genes and Progression of Lung Disease in Cystic Fibrosis

E Blue, TL Louie, JX Chong… - Annals of the …, 2018 - search.proquest.com
The observation that there is wide interindividual variation in severity of lung disease in
persons with the same cystic fibrosis transmembrane conductance regulator gene (CFTR) …

Variation in Cilia Protein Genes and Progression of Lung Disease in Cystic Fibrosis

E Blue, TL Louie, JX Chong… - Annals of the …, 2018 - pubmed.ncbi.nlm.nih.gov
Rationale Cystic fibrosis, like primary ciliary dyskinesia, is an autosomal recessive disorder
characterized by abnormal mucociliary clearance and obstructive lung disease. We …

Variation in Cilia Protein Genes and Progression of Lung Disease in Cystic Fibrosis.

E Blue, TL Louie, JX Chong, SJ Hebbring… - Annals of the …, 2018 - europepmc.org
Rationale: Cystic fibrosis, like primary ciliary dyskinesia, is an autosomal recessive disorder
characterized by abnormal mucociliary clearance and obstructive lung disease. We …