Left ventricular noncompaction

YM Hoedemaekers, T Germans - Clinical Cardiogenetics, 2020 - Springer
… Becker muscular dystrophy and in myotonic dystrophy (see … with moderate risk for cardiac
events (modified WHO class II–… in two families with non-compaction cardiomyopathy: linking …

Understanding left ventricular hypertrabeculation/noncompaction: pathomorphologic findings and prognostic impact of neuromuscular comorbidities

C Stöllberger, J Finsterer - Expert Review of Cardiovascular …, 2019 - Taylor & Francis
… , and myotonic dystrophy type 1. LVHT does not seem to be a special type of cardiac …
volume quantification in patients with left ventricular non-compaction cardiomyopathy. Eur …

Comprehensive investigations are required to manage cardiac disease in myotonic dystrophy 2

J Finsterer - Acta Neurologica Belgica, 2020 - Springer
patients with myotonic dystrophy type 2 (MD2) for cardiac involvement [1]. Diastolic dysfunction
was found in 43.5% of the patients, … of the included patients presented with left ventricular

Left ventricular hypertrabeculation/noncompaction, cardiac phenotype, and neuromuscular disorders

C Stöllberger, C Wegner, J Finsterer - Herz, 2019 - search.proquest.com
… LVHT occurs in normally sized, well-contracting left ventricles as well as in dilated ventricles
with … and variable outcomes of isolated left ventricular non-compaction. Heart 93:65–71 …

Structural and electrical cardiac abnormalities are prevalent in asymptomatic adults with myotonic dystrophy

P Choudhary, R Nandakumar, H Greig, P Broadhurst… - Heart, 2016 - heart.bmj.com
Patients with MD had a significantly lower left ventricular (LV) … differ between patients with
non-compaction and patients with … delayed ventricular potentials due to non-compaction may …

[PDF][PDF] Left ventricular trabeculation and noncompaction cardiomyopathy: a review

SI McFarlane - EC clinical and experimental anatomy, 2019 - researchgate.net
ventricular chamber development and its association with congenital heart disease, namely
left ventricular (LV) non-compaction (… distributions like Myotonic dystrophies and Cobalamin …

Neuromuscular Disorders and Noncompaction Cardiomyopathy

J Finsterer, C Stöllberger - Noncompaction Cardiomyopathy, 2019 - Springer
… Expansion of this motif between >75 and up to 11,000 repeats causes myotonic dystrophy
type-2 (MD2) . MD2 is a multisystem disorder manifesting mainly in the muscle, eyes, and …

[HTML][HTML] Left ventricular noncompaction− Risk stratification and genetic consideration−

F Ichida - Journal of Cardiology, 2020 - Elsevier
… trained athletes [50], patients with myotonic dystrophy [51], and in the … reported that familial
left ventricular non-compaction is associated … may underlie myocardial non-compaction [57]. …

Left ventricular noncompaction cardiomyopathy: cardiac, neuromuscular, and genetic factors

J Finsterer, C Stoellberger, JA Towbin - Nature Reviews Cardiology, 2017 - nature.com
… , Barth syndrome, zaspopathy, myotonic dystrophy type 1, dystrobrevinopathy, and Emery–Dreifuss
muscular dystrophy owing to LMNA mutations 17 (Table 2). Arguments against a …

[PDF][PDF] Predictors of poor outcome in patients with left ventricular noncompaction: Review of the literature

M Kubik, A Dąbrowska-Kugacka… - Adv Clin Exp …, 2018 - ppm-system.gumed.edu.pl
patients meeting cardiovascular magnetic resonance criteria for isolated left ventricular
non-compaction. … with isolated left ventricular noncompaction. Am J Cardiol. 2012;109:276–281. …