Congenital surfactant protein B (SP-B) deficiency: a case report

F Khalsi, M Chaabene, MB Romdhane… - Pan African Medical …, 2023 - ajol.info
surfactant metabolism are a diverse group of rare and complex respiratory diseases. Our case
illustrates an early diagnosis of surfactant protein B deficiency … to be the future therapy but …

Genetic disorders of surfactant protein dysfunction: when to consider and how to investigate

A Gupta, SL Zheng - Archives of Disease in Childhood, 2017 - adc.bmj.com
… disease are surfactant protein B, surfactant protein C, ATP … Surfactant protein dysfunction
syndromes are highly variable … in future pregnancies and the availability of prenatal diagnosis if …

Surfactant protein B: From biochemistry to its potential role as diagnostic and prognostic marker in heart failure

C Banfi, P Agostoni - International journal of cardiology, 2016 - Elsevier
… regulation by glucocorticoids because they accelerate fetal lung development and surfactant
… Accordingly SP-B may in the near future become a marker to clinically follow alveolar …

Surfactant protein disorders in childhood interstitial lung disease

J Singh, A Jaffe, A Schultz, H Selvadurai - European Journal of Pediatrics, 2021 - Springer
Surfactant proteins, such as surfactant protein B and surfactant protein C, contribute to … In
terms of prospective treatments, recent studies in murine models have also shown encouraging …

Genetic surfactant dysfunction in newborn infants and children with acute and chronic lung disease

M Somaschini, S Presi, M Ferrari, B Vergani… - Journal of Pediatric and …, 2017 - jpnim.com
Prenatal diagnosis was performed in 8 women with a previous … Surfactant protein B (SP-B)
deficiency was the first … Beginning in 2004, ABCA3 analysis was performed prospectively and …

Surfactant status and respiratory outcome in premature infants receiving late surfactant treatment

PL Ballard, RL Keller, WE Truog, C Chapin… - Pediatric …, 2019 - nature.com
… of phospholipid, surfactant protein B, and total protein were … Surfactant production in fetal
life and at birth is directly related to … and worthy of exploring prospectively as a predictor. In …

Surfactant status assessment and personalized therapy for surfactant deficiency or dysfunction

D De Luca, B Loi, D Tingay, H Fiori, P Kingma… - Seminars in Fetal and …, 2023 - Elsevier
… discuss these diagnostic tools from a pathophysiological and multi-disciplinary perspective,
… ,[39] due to a relative surfactant dilution or under-expression of surfactant proteins.[93] The …

[HTML][HTML] Surfactant replacement therapy: from biological basis to current clinical practice

R Hentschel, K Bohlin, A van Kaam, H Fuchs… - Pediatric …, 2020 - nature.com
… the most promising aims for future development. Scientists have … of specific proteins, called
surfactant protein (SP)-A, -B, -C … of RDS antenatally, 9 need for intubation and surfactant early …

Can first trimester pregnancy-associated plasma protein-A predict the surfactant needs of preterm neonates?

B Yakistiran, MF Karsli… - … of Neonatal-Perinatal …, 2022 - content.iospress.com
… and surfactant protein, IGF-2 deficiency was shown to result in decreased airspace
formation in fetal lungs, less alveolar separation, decreased SP-A expression, increased SP-B

The role of surfactant therapy in nonrespiratory distress syndrome conditions in neonates

A Keiser, V Bhandari - American journal of perinatology, 2016 - thieme-connect.com
… a prenatal diagnosis of CDH did not have a statistically greater risk of death than postnatally
diagnosed … Who, when and how should we treat newborn infants in the future?. BMC Pediatr …