… of the disease. This review focuses on the lung involvement in cystic fibrosis and summarizes
new … of CF and pathogenesis of related lung disease. Current therapeutic modalities, novel …

Cystic fibrosis (CF) is a common, life-threatening, multisystemic, autosomal recessive disorder.
In the last few years, giant steps have been made with regard to the understanding of CF …

… Progressive lung disease in cystic fibrosis (CF) is the life-limiting factor of this autosomal …
of CF lung disease, hence longitudinal imaging is recommended for disease monitoring in the …

… of new therapeutics to treat bronchiectasis in cystic fibrosis can be maintained … lung function,
and evidence suggests that such endpoints are less responsive in the adult cystic fibrosis …

… of cystic fibrosis (CF) lung disease was focused on symptomatic treatment of chronic lung
infection… In this overview, the literature is reviewed on early stage CF lung disease from animal …

… While the quality of life and survival of individuals with cystic fibrosis (CF) are improving,
advanced CF lung disease (ACFLD) remains common and the most frequent cause of death. CF …

… Clearance Index may be a useful marker to track early disease progression and guide
therapies in young patients with cystic fibrosis. Cystic fibrosis (CF) lung disease begins early in life …

… understanding of the pathogenesis and progression of lung disease in cystic fibrosis (CF).
Pulmonary inflammation, infection, and structural lung damage manifest very early in life and …

… in early lung disease, a meeting of … Cystic Fibrosis Conference. The meeting entitiled ‘Shaping
imaging and functional testing for early disease detection of lung disease in Cystic Fibrosis…

… Cystic fibrosis (CF) is a multiorgan recessive genetic disease caused by mutations in the cystic
fibrosis … Gene therapy efforts have focused on treating the lung, since it manifests the most …