Background: Polycystic liver disease (PLD) is present in most patients with autosomal
dominant polycystic kidney disease (ADPKD). PLD can alternatively be found with few, if …

Background/Aims: Polycystic liver disease (PCLD), a dominantly inherited condition
separate from polycystic kidney disease (PKD), has recently been found to be linked to a …

Background Factors related to the development and severity of polycystic liver disease
(PLD) have not been well established. We aimed to evaluate the genetic and epidemiologic …

Polycystic liver disease (PCLD) is characterized by the growth of fluid-filled cysts of biliary
epithelial origin in the liver. Although the disease is often asymptomatic, it can, when severe …

The development of a polycystic liver is a characteristic of the monogenic disorders:
autosomal dominant polycystic kidney disease (ADPKD), autosomal recessive polycystic …

Polycystic liver disease (PLD) is proven to occur either sporadically or in association with
autosomal dominant polycystic kidney disease (ADPKD), whereas the existence of an …

Adult polycystic disease of the liver (APLD) and of the kidney (ADPKD) is considered to
represent one entity. In 75 ADPKD kindreds with 259 affected members, ultrasonography …

Background The autosomal dominant polycystic kidney disease (APDKD) genotype
influences renal phenotype severity but its effect on polycystic liver disease (PLD) is …

Background Most patients with autosomal-dominant polycystic kidney disease (ADPKD)
develop liver cysts and polycystic liver disease as they age. To date, no simple clinical …

SG We still do not have a clear definition of this disease, although a recent consensus
statement defined it as the presence of more than 10 fluid-filled cysts within the liver …