… and pathological heterogeneity of the various FTLD subtypes… in atypical frontotemporal
lobar degeneration with ubiquitin-… FUS pathology that characterizes the three major FTLD-FUS …

… A pathological classification of FTLD is based on the … Four different subtypes of FTLD-TDP
(from A to D) have been … fifth subtype (FTLD-TDP type E) with distinctive pathological features …

… with FUS pathology has yet been associated with a FUS … in ALS-FUS cases only contain
FUS protein, FUS-positive … -TDP subtype B pathology with absence of any FET pathology …

… cause of frontotemporal dementia characterized by fused in sarcoma-positive inclusions.
It is classified as a subtype of frontotemporal lobar degeneration with FUS pathology. Cases …

… with a specific pathology and subtypes of each pathology as well as … A less common pathology
is FTLD related to FUS–Ewing … is that each of these pathological entities tends to occur in …

… selective degeneration of the frontal and temporal lobes is a consistent feature and “frontotemporal
lobar degeneration” (FTLD) is used as the generic term for those pathologies that …

… These features led to a neuropathological diagnosis of frontotemporal lobar degeneration
… However, no mutations have yet been linked with the FTLD-FUS histological subtype (which …

… been suggested that a UPS failure could be involved in the pathophysiology of the disease
[38, 49]. In … Analyzing FLTD subtypes, we observed that FTLD-FUS shows a more substantial …

… Frontotemporal lobar degeneration (FTLD) is associated with … ), or fused in sarcoma protein
(FUS). There have been very few … different clinical subtypes and pathological subtypes. This …

… PPA cases have AD as the underlying pathology. Moreover, patients in a prodromal stage …
FTLD subtypes. Incidence rates were computed as the ratio of the number of new FTLD cases …