… Inherited syndromes are important to recognize in the setting of a pancreatic neuroendocrine
… Although most PNETs are sporadic, approximately 10% are due to an inherited syndrome, …

… Neuroendocrine neoplasms can occur as part of inherited disorders, usually in the form of …
inherited syndromes with a special focus on molecularly targeted therapies for these lesions. …

… Recent evidence also suggests high-grade neuroendocrine neoplasms including NECs and
grade 3 NET can … This section of the chapter focuses on inherited epithelial pituitary NENs. …

… Pancreatic neuroendocrine neoplasms (PanNENs) are the neuroendocrine neoplasms
with … Approximately 10% of PanNENs arise as inherited tumour syndromes which include …

… In addition, these neuroendocrine neoplasms are capable of … tumors present as parts on
inherited genetic syndromes, such … Neoplasms of the neuroendocrine pancrea (panNEN) are a …

… to neuroendocrine neoplasms (NENs) in the 2022 WHO Classification of Endocrine and
Neuroendocrine Tumors. … from epithelial neoplasms, which are divided into well-differentiated …

… of neuroendocrine neoplasms comprises a heterogeneous group of tumors arising from
neuroendocrine … Approximately 20% of endocrine neoplasms are due to inherited syndromes, …

… Neuroendocrine neoplasms (NENs) have been primarily … subset of pancreatic neuroendocrine
neoplasms, including BRCA2… association between NENs and inherited (germline) PALB2, …

… advances in the pathobiology of pancreatic neuroendocrine neoplasms (PanNENs), and …
well-differentiated neuroendocrine tumor (PanNET) and poorly differentiated neuroendocrine …

… inherited endocrine neoplasia of the pituitary, thyroid, parathyroid, and adrenal glands, as
well as neuroendocrine … Confirmation of an inherited endocrine neoplasia condition provides …