… , Charcot–Marie–Tooth, Emery–Dreifuss muscular dystrophy, myotonic dystrophy, Leber’s …
valuation of the left ventricular function in patients in whom the hypertrabeculation was found …

Aims To assess the reported prevalence of left ventricular non-compaction (LVNC) in
different adult cohorts, taking in to consideration the role of diagnostic criteria and imaging …

… , alpha cardiac actin, cardiac troponin T • Acquired hypertrabeculation or noncompaction
has been reported in association with neuromuscular disorders and myotonic dystrophies [3]. …

Background Left ventricular noncompaction (LVNC) is a structural abnormality of the left
ventricular myocardium of unknown cause. Cardiovascular system involvement is an important …

… , myotonic dystrophy type 1, dystrobrevinopathy, and Emery-Dreifuss muscular dystrophy. …
imaging showing hypertrabeculation mostly affecting the left ventricular apical region and …

… Left ventricular noncompaction is a poorly defined and … of hypertrabeculation, which have
low specificity for identifying true cardiomyopathy cases. The management of left ventricular …

… hypertrabeculation contributes to disease and whether left … of the left ventricle wall in
conjunction with left ventricular (LV) … to compact myocardium of at least 2:1 (the NC/C ratio). The …

… A variety of neuromuscular disorders, such as myotonic dystrophy or amyloidosis, may …
hypertrabeculated layer and deep recesses communicating with the left ventricular cavity and an …

… in patients with myotonic dystrophy type 1 (MD1), an autosomal dominant type of disorder
… to be in association with left ventricular hyper trabeculation and some clinical conditions. …

… A specific NMD was diagnosed in 21 (metabolic myopathy in 14, Leber’s hereditary optic
neuropathy in 3, myotonic dystrophy in 2, Becker muscular dystrophy in 1 and DMD in 1, …