Recurrent C3 Glomerulonephritis with an ADAMTS 13 Gene Variant: A Case Report and Literature Review

RA Al Zahrani, AMAY Nazmi… - Saudi Journal of Kidney …, 2021 - journals.lww.com
C3 glomerulonephritis (C3GN) and dense deposit disease (DDD).[ 1 ] Abnormal control of
the alternative pathway (AP) has emerged as a risk factor for … , the primary disease took 84 …

Autoimmune abnormalities of the alternative complement pathway in membranoproliferative glomerulonephritis and C3 glomerulopathy

M Noris, R Donadelli, G Remuzzi - Pediatric Nephrology, 2019 - Springer
… and not with the isolated C3 convertase proteins or fragments [… glomerulonephritis
characterised by glomerular C3 deposits … a primary hit and/or other genetic or acquired …

Outcome of C3 glomerulopathy patients: Largest single-centre experience from South Asia

A Kumar, R Nada, R Ramachandran, A Rawat… - Journal of …, 2020 - Springer
… Limited genetics workup for CFH and CFHR5 genes was … we need to identify the potential
risk factors/triggers in our C3G … , c immunoflurescence showing massive C3 deposits along the …

[HTML][HTML] Clinical and pathophysiological insights into immunological mediated glomerular diseases in childhood

A Mastrangelo, J Serafinelli, M Giani… - Frontiers in Pediatrics, 2020 - frontiersin.org
… in the context of primary or systemic disease. In particular, … mediated primitive forms of
glomerulonephritis, together with … the pathological entities characterized by isolated C3 deposits, …

Diagnostic Challenges and Emerging Pathogeneses of Selected Glomerulopathies

NK Andeen, J Hou - Pediatric and Developmental Pathology, 2024 - journals.sagepub.com
… displays differences from a primary MN pattern, including … (Figure 6) and lupus nephritis,
entities for which it has only slightly … in cases with isolated C3 glomerular deposits confirmed its …

[HTML][HTML] Efficacy of eculizumab in coexisting complement C3 glomerulopathy and atypical hemolytic uremic syndrome

M Busutti, F Diomedi-Camassei, R Donadelli… - Kidney International …, 2021 - Elsevier
… of the glomerular C3 deposits allows distinction into 2 subtypes, C3 glomerulonephritis and
… travel expenses or financed a patient nonprofit organization and in no way influenced the …

Standardized classification and reporting of glomerulonephritis

S Sethi, FC Fervenza - Nephrology Dialysis Transplantation, 2019 - academic.oup.com
C3 glomerulopathy are specific diseases in themselves, while monoclonal Ig GN includes
proliferative GN with monoclonal Ig deposits and monoclonal Ig deposition disease… the primary

A definition, modern classification, and global epidemiology of primary glomerulonephritis

C Ponticelli, RJ Glassock - … of Primary Glomerulonephritis, 2019 - books.google.com
Primary glomerulonephritis with isolated C3 deposits: A new entity which shares
common genetic risk factors with haemolytic uraemic syndrome. J Med Genet. 44: 193–9. …

Inherited kidney complement diseases

M Lemaire, D Noone, AL Lapeyraque… - Clinical Journal of the …, 2021 - journals.lww.com
… In isolation, each method has its limitations, and an abnormal … of postinfectious
glomerulonephritis. CFB, complement … , with variable immune complex deposits (but no C3

C3 Glomerulopathy with concurrent thrombotic microangiopathy: clinical and immunological features

M Chabannes, M Rabant, C El Sissy… - American Journal of …, 2023 - Elsevier
… in C3GN and aHUS suggests a pathophysiological continuum between the 2 entities… and
subendothelial C3 deposits (anti-C3 fluorescein isothiocyanate-… Haemolytic uraemic syndrome