… of the disease. This review focuses on the lung involvement in cystic fibrosis and summarizes
new … of CF and pathogenesis of related lung disease. Current therapeutic modalities, novel …

Cystic fibrosis (CF) is a common, life-threatening, multisystemic, autosomal recessive disorder.
In the last few years, giant steps have been made with regard to the understanding of CF …

… of new therapeutics to treat bronchiectasis in cystic fibrosis can be maintained … lung function,
and evidence suggests that such endpoints are less responsive in the adult cystic fibrosis …

… in early lung disease, a meeting of … Cystic Fibrosis Conference. The meeting entitiled ‘Shaping
imaging and functional testing for early disease detection of lung disease in Cystic Fibrosis…

… While the quality of life and survival of individuals with cystic fibrosis (CF) are improving,
advanced CF lung disease (ACFLD) remains common and the most frequent cause of death. CF …

… Cystic fibrosis (CF) is a multiorgan recessive genetic disease caused by mutations in the cystic
fibrosis … Gene therapy efforts have focused on treating the lung, since it manifests the most …

… suppurative lung disease including bronchiectasis. It was then that the condition cystic fibrosis
… placed on treating undernutrition and progressive lung disease because of the associated …

… Cystic fibrosis (CF) is an autosomal recessive … lung disease of CF that causes the greatest
morbidity and mortality. The disease is caused by mutations of the CFTR (cystic fibrosis …

Background Airway infection leads to progressive damage of the lungs in cystic fibrosis (CF)
and oxidative stress has been implicated in the etiology. Supplementation of antioxidant …

… This review focusses on key findings from studies using candidate gene and genome-wide
approaches to identify CF modifier genes of lung disease in cystic fibrosis and considers the …