… Most children with cystic fibrosis (CF) in current times are likely … disease. Currently, such
individuals often present clinically as adults and are not necessarily given the full cystic fibrosis …

… Chronic airway colonisation by Pseudomonas aeruginosa, a hallmark of cystic fibrosis (CF)
lung disease, is associated with increased morbidity and mortality and despite aggressive …

… chloride anion channel, the cystic fibrosis transmembrane conductance regulator (CFTR).
The primary cause of morbidity and mortality is progressive lung disease due to thick, …

… in non-cystic fibrosis lung disease is presented in table 1. With further development, CFTR
modulators may prove to be a therapy for some lung diseases associated with acquired CFTR …

… Besides the disadvantage of the intestinal complication, as predicted, both pig models
spontaneously develop lung disease and present significant alterations of the pancreas and liver …

… Introduction Xenon-129 ( 129 Xe) ventilation magnetic resonance imaging (MRI) is sensitive
to detect early cystic fibrosis (CF) lung disease and response to treatment. Xe-MRI could …

… Cystic fibrosis (CF) is one of the most common life-shortening genetic diseases in Caucasians.
Due to abnormal accumulation of mucus, respiratory failure caused by chronic infections …

… There is emerging evidence for the role of posaconazole in the management of
Aspergillus-related cystic fibrosis (CF) lung disease. The tolerability and efficacy of posaconazole in …

… symptoms and signs that are considered to be non-typical for their clinical situation, the first
step is to exclude more common causes of chronic respiratory symptoms (ie, cystic fibrosis, …

… elastase (NE) is a major inflammatory protease released by neutrophils and is present in
the airways of patients with cystic fibrosis (CF), chronic obstructive pulmonary disease, non-CF …