Myotonic dystrophy type 1 (DM1) is the most common adult form of muscular dystrophy,
presenting with a constellation of systemic findings secondary to a CTG triplet expansion of …

Arrhythmias in Myotonic Dystrophy Patients Background Myotonic dystrophy (MD) is the
most common muscular dystrophy in adults and is associated with sudden death. Reported …

The myotonic dystrophies (types 1 and 2) are autosomal dominant, multisystem diseases
with relevancy to cardiac electrophysiologists because of the risk for arrhythmias. The more …

Myotonic dystrophies are pleiotropic diseases, dominantly inherited and affecting multiple
organ systems including the heart. Myotonic dystrophy has 2 major forms that differ …

Objective Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in
adults. DM1 is a multisystem disorder also affecting the heart with an increased incidence of …

Myotonic dystrophy is an autosomal dominant genetic disease of nucleotide expansion
resulting in neuromuscular disease with two distinct subtypes. There are significant systemic …

Background Patients with myotonic muscular dystrophy (dystrophia myotonica, DM) are at
risk of sudden cardiac death due to diverse arrhythmias, especially progressive …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

Background Cardiac involvement represents a major cause of morbidity and mortality in
patients with myotonic dystrophy type 1 (DM1) and prevention of sudden cardiac death …

Background: Patients with myotonic dystrophy (DM) have an annual mortality of
approximately 3.5%, one‐third of which is sudden cardiac death. The predictors of cardiac …