BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Abstract Introduction/Aims Type 1 myotonic dystrophy (DM1) is a neuromuscular disorder of
multiple organ systems with important electrophysiologic (EP) manifestations, leading to a …

Background Cardiac involvement in myotonic dystrophy type 1 (MD1) includes conduction
disease, arrhythmias, and left-ventricular (LV) systolic dysfunction leading to an increased …

Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …

Myotonic dystrophy is an inherited systemic disorder affecting skeletal muscle and the heart.
Genetic testing for myotonic dystrophy is diagnostic and identifies those at risk for cardiac …

Background: Conduction and ventricular arrhythmic disturbances in myotonic dystrophy
(MD) are the main causes of cardiac morbidity and mortality. Methods: To better define the …

Pacemakers and ICDs in Myotonic Dystrophy. Introduction: We assessed implant rates,
indications, characteristics, and outcomes in patients with the neuromuscular disease …

Cardiac involvement is recorded in about 80% of patients affected by myotonic dystrophy
type 1 (DM1). The prevalence of cardiac conduction abnormalities and arrhythmias has …

Myotonic dystrophy type 1 (DM1), also called Steinert's disease, is a multisystemic disorder
for which the cardiologist is often consulted. Clinical manifestations of this disease, which …

Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in adults. It is a
multisystem disorder also aff ecting the heart with an increased incidence of sudden cardiac …