Background: Patients with myotonic dystrophy (DM) have an annual mortality of
approximately 3.5%, one‐third of which is sudden cardiac death. The predictors of cardiac …

Background Sudden death can occur as a consequence of cardiac-conduction
abnormalities in the neuromuscular disease myotonic dystrophy type 1. The determinants of …

Arrhythmias in Myotonic Dystrophy Patients Background Myotonic dystrophy (MD) is the
most common muscular dystrophy in adults and is associated with sudden death. Reported …

Background Myotonic dystrophy type 1 (DM1) has been associated with an increased risk of
sudden death, either by heart block or malignant ventricular arrhythmias. Identifying patients …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Objective Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in
adults. DM1 is a multisystem disorder also affecting the heart with an increased incidence of …

The aim of this study was to analyze survival, causes of death and cardiologic predictors of
sudden death in a large cohort of patients with myotonic dystrophy type 1 (DM1). The study …

OBJECTIVE: The aim of the study was to identify, in addition to conduction defects, possible
predictors of cardiac events and death in patients with myotonic dystrophy (DM1) …

Aims To describe the incidence and identify predictors of sudden death (SD), major
conduction defects and sustained ventricular tachyarrhythmias (VTA) in myotonic dystrophy …