Surfactant Protein Deficiency Syndrome in Childhood Interstitial Lung Disease

J Singh, A Jaffe, A Schultz… - Authorea Preprints, 2020 - advance.sagepub.com
Surfactant, which was first identified in the 1920s is pivotal to lower the surface tension in
alveoli of the lungs and helps to lower the work of breathing and prevents atelectasis …

Surfactant protein disorders in childhood interstitial lung disease

J Singh, A Jaffe, A Schultz, H Selvadurai - European Journal of Pediatrics, 2021 - Springer
Surfactant, which was first identified in the 1920s, is pivotal to lower the surface tension in
alveoli of the lungs and helps to lower the work of breathing and prevents atelectasis …

Evaluation and management of inherited disorders of surfactant metabolism

H Aaron - Chinese medical journal, 2010 - mednexus.org
Objective To review the pathophysiology, evaluation, management, and outcomes of
children with inherited disorders of surfactant metabolism due to mutations in the genes …

Lung diseases associated with inherited disorders of surfactant metabolism

R Epaud, D Feldmann, L Guillot… - Archives de Pediatrie …, 2008 - europepmc.org
Lung diseases associated with surfactant-metabolism disorders are a heterogeneous group
of rare diseases. Intra-alveolar accumulation of protein related to surfactant dysfunction …

Persistent respiratory distress in the term neonate: genetic surfactant deficiency diseases

JE Magnani, SM Donn - Current pediatric reviews, 2020 - ingentaconnect.com
Respiratory distress is one of the most common clinical presentations in newborns requiring
admission to a Neonatal Intensive Care Unit (NICU). Many of these infants develop …

TOTAL VIEWS

M Silahli, Z Gökmen - hillpublisher.com
Surfactants are surface-active agents lowering surface tension in the airways of the lung. It
plays an important role on pulmonary function. Surfactant proteins constitute 10 percent of …

TOTAL VIEWS: 6148

M Silahli, Z Gökmen - hillpublisher.com
Surfactants are surface-active agents lowering surface tension in the airways of the lung. It
plays an important role on pulmonary function. Surfactant proteins constitute 10 percent of …

Genetic disorders of surfactant protein dysfunction: when to consider and how to investigate

A Gupta, SL Zheng - Archives of Disease in Childhood, 2017 - adc.bmj.com
Genetic mutations affecting proteins required for normal surfactant protein function are a rare
cause of respiratory disease. The genes identified that cause respiratory disease are …

TOTAL VIEWS: 6136

M Silahli, Z Gökmen - hillpublisher.com
Surfactants are surface-active agents lowering surface tension in the airways of the lung. It
plays an important role on pulmonary function. Surfactant proteins constitute 10 percent of …

Surfactant proteins in pediatric interstitial lung disease

M Griese, E Lorenz, M Hengst, A Schams… - Pediatric …, 2016 - nature.com
Background: Children's interstitial lung diseases (chILD) comprise a broad spectrum of
diseases. Besides the genetically defined surfactant dysfunction disorders, most entities …