[HTML][HTML] Cystic fibrosis related liver disease and endocrine considerations

JS Sherwood, J Ullal, K Kutney, KS Hughan - Journal of Clinical & …, 2022 - Elsevier
… The multi-center PUSH study (Prediction by Ultrasound of the Risk of Hepatic Cirrhosis in
Cystic Fibrosis) demonstrated that a heterogenous pattern on ultrasound predicts progression …

[HTML][HTML] The impact of liver disease on mortality in cystic fibrosis–a systematic review

A Sasame, D Stokes, B Bourke, L Connolly… - … of Cystic Fibrosis, 2022 - Elsevier
… The Dutch CF Registry was used to generate a comparator group of participants over 8 years
of age with no liver disease while those with Cystic Fibrosis Cirrhosis (CFC) were attending …

Cystic fibrosis-related liver disease is associated with increased disease burden and endocrine comorbidities

H Singh, MJ Coffey, CY Ooi - Journal of Pediatric …, 2020 - journals.lww.com
liver biopsy and were confirmed to have cirrhosis compared with those with cirrhosis-like …
hyperplasia or portal hypertension without cirrhosis from portal obliterative venopathy (26) . …

epidemiology, pathogenesis and management of liver disease in adults with cystic fibrosis

J Scott, AM Jones, K Piper Hanley… - Alimentary …, 2022 - Wiley Online Library
… -cirrhotic CFLD and no liver disease. The diagnostic range reported as a cut-off for CFLD
varies and appears much lower than other causes of cirrhosis. … liver fibrosis in fatty liver disease

Cystic fibrosis-related liver disease: clinical presentations, diagnostic and monitoring approaches in the era of CFTR modulator therapies

J Dana, D Debray, A Beaufrère, S Hillaire, M Fabre… - Journal of …, 2022 - Elsevier
… , liver involvement in these patients is not always CF-related liver disease (CFLD) which only
includes disease … : multilobular cirrhosis with or without portal hypertension or liver failure, …

Current treatment options for cystic fibrosis-related liver disease

K Staufer - International journal of molecular sciences, 2020 - mdpi.com
… to current guidelines on patients with decompensated liver cirrhosis [28]. However, it needs
… of liver cirrhosis and the presence of preserved liver function [29]. Non-cirrhotic portal …

Non-cirrhotic portal hypertension (obliterative portal venopathy) is the predominant form of chronic liver disease in cystic fibrosis

JP ONeill, CS Clifford, NP Nolan… - Irish Journal of Medical …, 2023 - Springer
… the liver pathology of end stage cystic fibrosis liver disease is quite different from that of the
classical biliary diseases, … Cirrhosis is uncommon in cystic fibrosis patients and instead the …

Serum bile acids in cystic fibrosis patients–glycodeoxycholic acid as a potential marker of liver disease

S Drzymała-Czyż, K Dziedzic, A Szwengiel… - … and Liver Disease, 2022 - Elsevier
… In our study, CF patients with liver disease (liver cirrhosis or other liver diseases) showed
significantly higher concentrations of primary, secondary and conjugated bile acids compared …

Heterogeneous liver on research ultrasound identifies children with cystic fibrosis at high risk of advanced liver disease: interim results of a prospective observational …

MJ Siegel, AJ Freeman, W Ye, JJ Palermo… - The Journal of …, 2020 - Elsevier
… ultrasound pattern pattern is recognized as a finding of advanced liver disease, such as
cirrhosis, on research ultrasound examination. Second, our follow-up is shorter than that …

Liver Disease in Cystic Fibrosis

C Colombo, PM Battezzati, C Fredella… - … of Biliary Epithelia, 2020 - taylorfrancis.com
… suggests that liver disease in CF is in different ways related … with Cystic Fibrosis: possible
relation to focal biliary cirrhosis. … development of cirrhosis: an autopsy study in Cystic Fibrosis. …