Left ventricular noncompaction

YM Hoedemaekers, T Germans - Clinical Cardiogenetics, 2020 - Springer
… Becker muscular dystrophy and in myotonic dystrophy (see … with moderate risk for cardiac
events (modified WHO class II–… in two families with non-compaction cardiomyopathy: linking …

Comprehensive investigations are required to manage cardiac disease in myotonic dystrophy 2

J Finsterer - Acta Neurologica Belgica, 2020 - Springer
patients with myotonic dystrophy type 2 (MD2) for cardiac involvement [1]. Diastolic dysfunction
was found in 43.5% of the patients, … of the included patients presented with left ventricular

[HTML][HTML] Left ventricular noncompaction− Risk stratification and genetic consideration−

F Ichida - Journal of Cardiology, 2020 - Elsevier
… trained athletes [50], patients with myotonic dystrophy [51], and in the … reported that familial
left ventricular non-compaction is associated … may underlie myocardial non-compaction [57]. …

[HTML][HTML] The relationship between takotsubo syndrome, left ventricular hypertrabeculation/noncompaction, neurologic and neuromuscular disorders

C Stöllberger, J Finsterer - Reviews in Cardiovascular Medicine, 2021 - imrpress.com
… Most frequently associated with LVHT are mitochondrial disorders, Barth syndrome, zaspopathy,
myotonic dystrophy type 1, dystrobrevinopathy and Emery-Dreifuss muscular dystrophy

A rare case report of severe cardiomyopathy associated with myotonic dystrophy type 2

AM Touma, PS Nijjar, GE Manousakis… - European Heart …, 2022 - academic.oup.com
… confirmed a severely enlarged left ventricular cavity with a left ventricular ejection fraction of
… -septal LGE by CMR and LV non-compaction which is often associated with neuromuscular …

[HTML][HTML] Left ventricular noncompaction: a disorder with genotypic and phenotypic heterogeneity—a narrative review

K Hirono, F Ichida - Cardiovascular Diagnosis and Therapy, 2022 - ncbi.nlm.nih.gov
Left ventricular noncompaction (LVNC), also used synonymously as hypertrabeculation, is a
cardiomyopathy characterized morphologically by two … to the left ventricular (LV) cavity (1,2). …

Noncompaction Cardiomyopathy: Issues, Contradictions, and Search for Effective Diagnostic Criteria. Literature Review. Part 1

AV Korotkikh, YV Vakhnenko, AN Kazantsev… - Current Problems in …, 2023 - Elsevier
… follow-up of 7 male patients with left ventricular myocardial … neuropathy, myotonic dystrophy,
Becker muscular dystrophy, … Symptoms of CHF at the same time regressed to class II. The …

Genetic basis of left ventricular noncompaction

P Rojanasopondist, L Nesheiwat… - Circulation: Genomic …, 2022 - Am Heart Assoc
Left ventricular noncompaction is a rare cardiomyopathy that is morphologically … 3 8.5
5.5 2 7.5 Moderate Mitochondrial complex V (ATP synthase) deficiency, nuclear type 2

A systematic review and meta-analysis of the prevalence of left ventricular non-compaction in adults

SB Ross, K Jones, B Blanch, R Puranik… - European Heart …, 2020 - academic.oup.com
Left ventricular non-compaction (LVNC) is described as a … Left ventricular non-compaction
was classified as a primary cardiomyopathy by the American Heart Association in 2006, 2

Overlap phenotypes of the left ventricular noncompaction and hypertrophic cardiomyopathy with complex arrhythmias and heart failure induced by the novel truncated …

Y Lin, J Huang, Z Zhu, Z Zhang, J Xian, Z Yang… - Orphanet Journal of …, 2021 - Springer
… The left ventricular noncompaction cardiomyopathy (LVNC) is a rare subtype of cardiomyopathy
(CM) and is characterized by predominant left ventricular trabeculations with deep …