… ADAMTS13 forming immune complexes, or if the assay used is not sensitive. Persistent
ADAMTS13 deficiency … as they transit through the partially obstructed glomerular capillaries. The …

… hemolytic uremic syndrome such as diacylglycerol kinase epsilon mutations or cobalamin C
deficiency … ADAMTS13, A disintegrin and metalloproteinase with a thrombospondin type 1 …

… The diagnosis of aHUS is made by the presence of TMA with normal ADAMTS13 activity
without … So far, the lack of an objective diagnostic tool makes diagnosing aHUS challenging. …

… Hemolytic uremic syndrome (HUS) is defined by the triad of microangiopathic hemolytic …
Such a variant of ADAMTS13 gene is frequently observed among patients with aHUS in our …

… of STEC infection, severe ADAMTS13 deficiency, or hyperhomocysteinemia/methyl-malonic …
of onset, although plasma therapy induced complete or partial remission of 63%, 25%, 57%, …

… The lack of verotoxins from enterohemorrhagic Escherichia … the diagnosis of atypical
hemolytic-uremic syndrome. After the … of ADAMTS13 activity for atypical hemolytic uremic …

… with severe plasma ADAMTS13 deficiency (Figure 48.2). … has been determined, and the
enzyme has been partially … of children with atypical hemolytic uremic syndrome. J Pediatr. …

… ADAMTS13, MMACHC (cb1c deficiency), or genes encoding complement proteins) or acquired
(autoantibodies to ADAMTS13… with complete or partial remission (hematologic remission …

… a heterogeneous group of conditions, including atypical hemolytic uremic syndrome (aHUS).
The … , but were discontinued later on upon return of a normal ADAMTS13 activity assay. …

… 1.4) with a normal activated partial thromboplastin time and a … is, a score that predicts
ADAMTS13 deficiency, in suspected … Complement-mediated hemolytic uremic syndrome (HUS) …