Thrombotic Thrombocytopenic Purpura, Atypical Hemolytic Uremic Syndrome, and Spectrum of Thrombotic Microangiopathy
M Riedl Khursigara, S Benoit, CJ Patriquin… - Pediatric …, 2022 - Springer
… ADAMTS13 forming immune complexes, or if the assay used is not sensitive. Persistent
ADAMTS13 deficiency … as they transit through the partially obstructed glomerular capillaries. The …
ADAMTS13 deficiency … as they transit through the partially obstructed glomerular capillaries. The …
Typical and atypical hemolytic uremic syndrome in the critically ill
CL Manrique-Caballero… - Critical Care …, 2020 - criticalcare.theclinics.com
… hemolytic uremic syndrome such as diacylglycerol kinase epsilon mutations or cobalamin C
deficiency … ADAMTS13, A disintegrin and metalloproteinase with a thrombospondin type 1 …
deficiency … ADAMTS13, A disintegrin and metalloproteinase with a thrombospondin type 1 …
[HTML][HTML] Atypical hemolytic uremic syndrome: Consensus of diagnosis and treatment in Taiwan
MH Tseng, SH Lin, JD Tsai, MS Wu, IJ Tsai… - Journal of the Formosan …, 2023 - Elsevier
… The diagnosis of aHUS is made by the presence of TMA with normal ADAMTS13 activity
without … So far, the lack of an objective diagnostic tool makes diagnosing aHUS challenging. …
without … So far, the lack of an objective diagnostic tool makes diagnosing aHUS challenging. …
Atypical Hemolytic Uremic Syndrome (aHUS) and Adenosine Deaminase (ADA)-Deficient Severe Combined Immunodeficiency (SCID)—Two Diseases That …
A Bogdał, A Badeński, M Pac, A Wójcicka… - International Journal of …, 2021 - mdpi.com
… Hemolytic uremic syndrome (HUS) is defined by the triad of microangiopathic hemolytic …
Such a variant of ADAMTS13 gene is frequently observed among patients with aHUS in our …
Such a variant of ADAMTS13 gene is frequently observed among patients with aHUS in our …
[HTML][HTML] Consensus regarding diagnosis and management of atypical hemolytic uremic syndrome
H Lee, E Kang, HG Kang, YH Kim, JS Kim… - The Korean Journal …, 2020 - ncbi.nlm.nih.gov
… of STEC infection, severe ADAMTS13 deficiency, or hyperhomocysteinemia/methyl-malonic …
of onset, although plasma therapy induced complete or partial remission of 63%, 25%, 57%, …
of onset, although plasma therapy induced complete or partial remission of 63%, 25%, 57%, …
MULTIFACTORIAL ETIOLOGY OF ATIPICAL HEMOLYTIC UREMIC SYNDROME-CASE REPORT
J Skoric, MK Uzelac, A Kostic - Sanamed, 2024 - aseestant.ceon.rs
… The lack of verotoxins from enterohemorrhagic Escherichia … the diagnosis of atypical
hemolytic-uremic syndrome. After the … of ADAMTS13 activity for atypical hemolytic uremic …
hemolytic-uremic syndrome. After the … of ADAMTS13 activity for atypical hemolytic uremic …
Thrombotic Thrombocytopenic Purpura, Hemolytic–Uremic Syndrome, and HELLP
KR Baker - Critical Care Obstetrics, 2024 - Wiley Online Library
… with severe plasma ADAMTS13 deficiency (Figure 48.2). … has been determined, and the
enzyme has been partially … of children with atypical hemolytic uremic syndrome. J Pediatr. …
enzyme has been partially … of children with atypical hemolytic uremic syndrome. J Pediatr. …
Atypical Hemolytic Uremic Syndrome
M Malina, V Fremeaux-Bacchi, S Johnson - Pediatric Kidney Disease, 2023 - Springer
… ADAMTS13, MMACHC (cb1c deficiency), or genes encoding complement proteins) or acquired
(autoantibodies to ADAMTS13… with complete or partial remission (hematologic remission …
(autoantibodies to ADAMTS13… with complete or partial remission (hematologic remission …
Complement-Amplifying Conditions in Atypical Hemolytic Uremic Syndrome: A Canadian Case Series
CJ Patriquin, K Pavenski, J Garland… - … Health and Disease, 2022 - journals.sagepub.com
… a heterogeneous group of conditions, including atypical hemolytic uremic syndrome (aHUS).
The … , but were discontinued later on upon return of a normal ADAMTS13 activity assay. …
The … , but were discontinued later on upon return of a normal ADAMTS13 activity assay. …
Case Report: Microangiopathic Hemolytic Anemia With Normal ADAMTS13 Activity
N Osti, G Beschin, M Goldin, L Guidolin… - Frontiers in …, 2021 - frontiersin.org
… 1.4) with a normal activated partial thromboplastin time and a … is, a score that predicts
ADAMTS13 deficiency, in suspected … Complement-mediated hemolytic uremic syndrome (HUS) …
ADAMTS13 deficiency, in suspected … Complement-mediated hemolytic uremic syndrome (HUS) …