… , a locally aggressive or borderline tumor and a malignant … hemihypertrophy and
Beckwith-Wiedemann syndrome [56]. … alpha is no longer recommended by recent guidelines for …

… tumor, these cases included two cases of hemihypertrophy … -trophy and Beckwith-Wiedemann
syndrome, whereas … with predisposition syndromes generally undergo careful surveillance …

… Therefore, it is necessary to identify these syndromes as early … should suggest a genetic
predisposition to cancer include a … remains monitoring with radiological evaluation every 6–12 …

… is critical for understanding disease biology and therapeutic … Participation in surveillance
programs may allow for early tumor … tumors, including high-grade sarcomas as well as locally …

… An intensive protocol of surveillance is recommended in … Only a few percent of
Beckwith-Wiedemann syndrome cases, such … avoid unnecessarily intensive tumor surveillance. In …

… aniridia, macroglossia, hemihyperplasia, macrosomia, and … A discussion of detailed renal
function surveillance in … 11p15-related WT (Beckwith-Wiedemann spectrum), WT1 disorder, …

… not recommended, as cancer rarely develops here [121]. … surveillance program has shown
to detect hepatoblastomas at an early stage in patients with Beckwith−Wiedemann syndrome (…

… as well as opportunities for surveillance and risk-reducing interventions… Beckwith Wiedemann
syndrome Complex genetics and … Screening is generally recommended if the risk of cancer …

… In Beckwith-Wiedemann syndrome, ACC tumors exhibit … , hemihypertrophy) or Wilm’s tumor.
Patients with Lynch … doubling and TERT expression suggests the important role TERT plays …