… of the disease. This review focuses on the lung involvement in cystic fibrosis and summarizes
new … of CF and pathogenesis of related lung disease. Current therapeutic modalities, novel …

… of new therapeutics to treat bronchiectasis in cystic fibrosis can be maintained … lung function,
and evidence suggests that such endpoints are less responsive in the adult cystic fibrosis …

… in early lung disease, a meeting of … Cystic Fibrosis Conference. The meeting entitiled ‘Shaping
imaging and functional testing for early disease detection of lung disease in Cystic Fibrosis…

… suppurative lung disease including bronchiectasis. It was then that the condition cystic fibrosis
… placed on treating undernutrition and progressive lung disease because of the associated …

… While the quality of life and survival of individuals with cystic fibrosis (CF) are improving,
advanced CF lung disease (ACFLD) remains common and the most frequent cause of death. CF …

… This review focusses on key findings from studies using candidate gene and genome-wide
approaches to identify CF modifier genes of lung disease in cystic fibrosis and considers the …

… The lung clearance index (LCI) measured by the multiple breath washout (… lung disease
in children with cystic fibrosis. While LCI worsens during the preschool years in cystic fibrosis, …

… its dysregulation contributes to CF lung disease. We summarize the current knowledge and
provide an outlook on the therapeutic options to treat the CF lung disease. In particular, we …

… Cystic fibrosis (CF) is the most common genetic … of CF lung disease and participate in its
progression. Anti-inflammatory therapies are, therefore, of particular interest for CF lung disease. …

… lung disease or await lung transplantation. While the hope is that these drug compounds will
prevent lung … need to care for people with advanced lung disease. The focus of this review …