Creutzfeldt-Jakob disease (CJD) is a rare transmissible, neurodegenerative disorder with an
annual incidence of approximately 1-2 per million population. 1–3 CJD represents the most …

Abstract Background Indigenous Australians are at increased risk of developing dementia–
Alzheimer disease and mixed dementia diagnoses are the most common. While prion …

Abstract The Australian National Creutzfeldt-Jakob Disease Registry (ANCJDR) was
established in October 1993 after the identification of probable iatrogenic CJD in recipients …

Prion diseases are rare neurodegenerative disorders that always lead to death and that can
be transmissible under certain conditions. Although sporadic Creutzfeldt-Jakob's disease …

Creutzfeldt–Jakob disease (CJD) is a fatal disease caused by the accumulation of abnormal
prion proteins in neurological tissues. Routine notification data reveal that NSW has similar …

The story began in the 1920s when Creutzfeldt and Jakob described independently an
unusual fatal neurological disorder. 1, 2 Considerable disagreement still exists over the …

Australia-wide prospective surveillance of human transmissible spongiform
encephalopathies (TSEs) has been conducted by the Australian National Creutzfeldt-Jakob …

Creutzfeldt–Jakob disease (CJD) is a rare neurode-generative disorder with a clinical
presentation of dementia, myoclonus and progressive motor dysfunction leading to death …

Kingdom'. This novel human prion disease was unusual in that it affected young adults, with
a lengthy clinical illness characterised by psychiatric and sensory symptoms at onset with …

Creutzfeldt-Jakob disease (CJD) is a rare neurodegenerative human prion disease with a
worldwide incidence of 1-per-million. CJD typically is rapidly progressive and invariably …