Alagille syndrome (AGS) is an autosomal dominant disorder of chronic cholestasis
characterized by paucity of interlobular bile ducts. The condition has been described only as …

Background Alagille syndrome is a rare autosomal-dominant disorder, representing 10 to
15% of the causes of neonatal cholestasis with no gender predominance. The diagnosis is …

Background Alagille syndrome, a rare genetic disorder with autosomal dominant
transmission, manifests with five major features: paucity of interlobular bile ducts …

Background: Alagille Syndrome is a rare genetic disease characterized by abnormalities of
the intrahepatic biliary ducts with cholestasis along with multisystem anomalies. Case …

Background Alagille syndrome (AS) is regarded as the most common cause of chronic
cholestasis in childhood associated with specific phenotypic features in western countries …

BACKGROUND: Alagille syndrome (AGS) is a dominantly inherited developmental disorder
with variable expression of five cardinal features: chronic cholestasis with bile duct paucity …

Objective: The aim of the study was to study the clinical and histological features of Alagille
syndrome (AGS) at presentation comparing the value of the various modalities before the …

Alagille syndrome (AGS) is one of the major forms of chronic liver disease in childhood with
severe morbidity and a mortality of 10 to 20%. It is characterised by cholestasis of variable …

Alagille syndrome (ALGS) is an autosomal dominant, multisystem disorder with variable
phenotypic penetrance that was first described in 1969 by Daniel Alagille. Initial diagnosis …

Alagille syndrome and progressive familial intrahepatic cholestasis are conditions that can
affect multiple organs. Advancements in molecular testing have aided in the diagnosis of …