Rationale: Criteria for progressive pulmonary fibrosis (PPF) have been proposed, but their
prognostic value beyond categorical decline in FVC remains unclear. Objectives: To …

Background Idiopathic pulmonary fibrosis (IPF) is a progressive disease with a variable
clinical course and high mortality. We used data from a large national US registry of patients …

Background Idiopathic pulmonary fibrosis (IPF) is a progressive and fatal fibrosing lung
disease of unknown cause. The advent of anti-fibrotic medications known to slow disease …

Background Patients with fibrotic interstitial lung disease (ILD) exhibit heterogeneous
disease courses, with idiopathic pulmonary fibrosis (IPF) being the prototypic subtype with a …

Emerging data show similarities in prognosis between patients with IPF or with non-IPF PF-
ILD patients. Early detection and appropriate treatment of this group of patients is a priority …

Background Proposed criteria for progressive fibrosing interstitial lung disease (PF-ILD)
have been linked to increased mortality risk, but lung function trajectory after satisfying …

Idiopathic pulmonary fibrosis (IPF) is a progressive and devastating disease with a median
survival time of 2–3 years after diagnosis. Patients with IPF exhibit distinct patterns of …

The American Thoracic Society and European Respiratory Society guidelines for the
diagnosis and treatment of idiopathic pulmonary fibrosis (IPF) have been published recently …

Of patients awaiting lung transplantation, the death rates are highest in those with idiopathic
pulmonary fibrosis (IPF), suggesting that many IPF patients are referred late for …

Introduction Prognostic factors of idiopathic pulmonary fibrosis (IPF) currently recognized
include changes in vital capacity and radiologic findings. However, most of the prognostic …