… in up to 80% of the cases [1] . LVHT has been reported in association with Duchenne or
Becker muscular dystrophy, myotonic dystrophy type 1, dystrobrevinopathy, Pompe’s disease, …

… , Charcot–Marie–Tooth, Emery–Dreifuss muscular dystrophy, myotonic dystrophy, Leber’s …
valuation of the left ventricular function in patients in whom the hypertrabeculation was found …

… of ventricular hypertrabeculation. Perfusion of the noncompact layer is typically worse
than perfusion of the compact layer, 55 which has been demonstrated on cardiac magnetic …

… of dystrophin, and endomyocardial biopsy is used to detect fibrosis, left ventricular
hypertrabeculation… Myotonic dystrophy type 1 (DM1), also known as Steinert’s disease, affects …

… (CMPs) include left ventricular hypertrabeculation or … , myotonic dystrophies, zaspopathies,
laminopathies, dystrobrevinopathies, oculopharyngeal muscular dystrophy, tropomyosin-1 …

… The combined prevalence of types 1 and 2 myotonic dystrophy is estimated to be 1 in 8000.
There is a wide variability in prevalence in different populations. There is higher prevalence …

… right than in the left ventricle. The proportion of the normal ventricular wall formed by …
Cardiac involvement in myotonic dystrophy, Becker muscular dystrophy and mitochondrial …

… (including mitral valve prolapse) and left ventricular hypertrabeculation (LVHT). Mitral valve
prolapse … dystrophy and myotonic dystrophy. 7th–9th June 2002. Naarden, The Netherlands. …

… Left ventricular noncompaction/hypertrabeculation is a … HCM, 3 whereas myotonic dystrophy
1 has been reported only … effects of the angiotensin II type 1 receptor blocker on myopathy in …

… Left ventricular noncompaction is a rare cardiomyopathy that is morphologically characterized
by … Left ventricular noncompaction (LVNC) is the third most common cardiomyopathy in the …