… Left ventricular noncompaction/hypertrabeculation is a … HCM, 3 whereas myotonic dystrophy
1 has been reported only … effects of the angiotensin II type 1 receptor blocker on myopathy in …

… of ventricular hypertrabeculation. Perfusion of the noncompact layer is typically worse
than perfusion of the compact layer, 55 which has been demonstrated on cardiac magnetic …

… Left ventricular noncompaction is a rare cardiomyopathy that is morphologically characterized
by … Left ventricular noncompaction (LVNC) is the third most common cardiomyopathy in the …

… Transmural fibrosis in the lateral free wall of the left ventricle … diagnosed with type 1 and type
2 myotonic dystrophy and … in patients affected with type 2 myotonic dystrophy and preserved …

… , left ventricular noncompaction cardiomyopathy has been described in patients with … in
the myotonic dystrophy protein kinase, the genetic basis for myotonic dystrophy type 1. …

… The combined prevalence of types 1 and 2 myotonic dystrophy is estimated to be 1 in 8000.
There is a wide variability in prevalence in different populations. There is higher prevalence …

… , also known as noncompaction cardiomyopathy [1]) is a complex … spongy myocardium or
hypertrabeculation syndrome but … Pronounced hypertrabeculation may be the result of altered …

… Duchenne or Becker muscular dystrophy, myotonic dystrophy type 1, dystrobrevinopathy, …
with cardiac involvement, particularly in myotonic dystrophy, it appears essential to investigate …

… ) was not yet known [1]. Historically, cases with an embryonic spongy pattern of the left
ventricle (LV) were … Ultrastructural investigations of hearts with noncompaction/hypertrabeculation …

… of left ventricular myocardium (… a left ventricular hypertrabeculation (VI) with deep
intertrabecular recesses communicating with the ventricular cavity directly but not coronary …