过去一年中添加的文章,按日期排序

C3 Glomerulopathy: A Kidney Disease Mediated by Alternative Pathway Deregulation

PF Zipfel, K Heidenreich, D Goel, PS Priyamvada… - Frontiers in … - frontiersin.org
4 天前 - C3 glomerulopathy (C3G) is an ultra-rare complement-mediated kidney disease due
to deregulation of the Alternative Pathway (AP) of proximal complement. Consequently, all …

C3 glomerulonephritis associated with monoclonal gammopathy of renal significance: a diagnostic and therapeutic challenge

B Beirão, M Freitas, N Silva, P Ferraz… - Brazilian Journal of …, 2024 - SciELO Brasil
5 天前 - … . The best example of a MGRS-associated disorder with absent or scant monoclonal
Ig deposition is C3 glomerulopathy (C3G), including dense deposit disease (DDD) and …

Successfully treated C3 glomerulopathy in which protein and genetic analyses were useful for diagnosis

M Kanzaki, M Kurahashi, K Watanabe, M Nishikawa… - CEN Case Reports, 2024 - Springer
8 天前 - … and is characterized by C3 deposition in the … against C3 or C5 converting enzyme
(convertase) and other complement-related proteins. We report a case of C3 glomerulopathy

V-210.1: Efficacy of 12-week pegcetacoplan in kidney transplant recipients with recurrent C3 glomerulopathy (C3G) or immune complex membranoproliferative …

A Bomback, E Daina, J Kanellis, D Kavanagh… - …, 2024 - journals.lww.com
20 天前 - … eGFR, targeted the pathophysiology of C3 dysregulation, and was well tolerated …
C3 and a reduction of plasma sC5b9 levels is consistent with the decreased breakdown of C3

[HTML][HTML] How Stem and Progenitor Cells Can Affect Renal Diseases

F Montenegro, F Giannuzzi, A Picerno, A Cicirelli… - Cells, 2024 - mdpi.com
22 天前 - … Consequently, an optimal therapeutic treatment for C3 glomerulopathy has not yet
been … to offer more effective and enduring treatments to patients with C3 glomerulopathy. …

Glomerular injury induced by vinyl carbamate in A/J inbred mice: a novel model of membranoproliferative glomerulonephritis

AY Gong, YJ Qiao, M Chen, Z Alam… - Frontiers in …, 2024 - frontiersin.org
33 天前 - … DDD and C3 glomerulonephritis now constitutes the two subgroups of C3
glomerulopathy. … deposition of granular C3. This pathologic pattern of glomerular injury is more …

Monoclonal gammopathy of renal significance from the perspective of nephrologists

K Park, SH Kwon - Blood research, 2024 - Springer
39 天前 - C3 glomerulopathy is characterized by dominant C3 deposits with a
membranoproliferative pattern. In C3 glomerulopathy, … of C3 convertase [20, 21]. This results in …

Corrigendum: Genetic investigation of Nordic patients with complement-mediated kidney diseases

V Rydberg, SS Aradottir, AC Kristoffersson… - Frontiers in …, 2024 - frontiersin.org
44 天前 - … Under the heading C3, rowc.4030-4C>G was under the ACMG classification stated
as “… The C3 level of patient 314 was given as “normal” when it should have been written as “…

Kidney transplantation in children and adolescents with C3 glomerulopathy or immune complex membranoproliferative glomerulonephritis: a real-world study within …

C Patry, NJA Webb, M Feißt, K Krupka, J Becker… - Pediatric …, 2024 - Springer
44 天前 - … over 60 months post-transplant in patients with C3 glomerulopathy (n = 17) or immune
… -transplant in the three subgroups of patients with C3 glomerulonephritis (C3GN, n = 12), …

Functional MRI to monitor disease progression in patients with rare kidney disease

A Caroli, G Villa, E Daina, P Brambilla, S Gamba… - archive.ismrm.org
50 天前 - … Keywords: Kidney, Quantitative ImagingThis study investigates the correlation
between MRI and histologic and clinical findings in 7 patients with C3 glomerulopathy and …