Idiopathic pulmonary fibrosis is a devastating, age-related lung disease of unknown cause
that has few treatment options. This disease was once thought to be a chronic inflammatory …

… Many forms of idiopathic interstitial pneumonia other than idiopathic pulmonary fibrosis have
… favorable prognosis and response to therapy than does idiopathic pulmonary fibrosis. The …

… and treatment options available for patients with idiopathic pulmonary fibrosis. This disease
has improved understanding of the mechanisms of lung fibrosis, and offers hope that similar …

… In this patient, who had no systemic disease or exposures that would exclude idiopathic
disease, the diagnosis of idiopathic pulmonary fibrosis (IPF) is certain. By contrast, the second …

… Regardless of the exact prevalence of each condition, idiopathic pulmonary fibrosis, chronic
hypersensitivity pneumonitis, connective-tissue disease–related ILD (CTD-ILD), and pulmonary …

… The largest description of familial pulmonary fibrosis identified 111 families with … idiopathic
interstitial pneumonia was present. This finding in particular suggests that pulmonary fibrosis, …

Idiopathic pulmonary fibrosis (IPF) is an interstitial lung disease characterised by chronic,
progressive scarring of the lungs and the pathological hallmark of usual interstitial pneumonia. …

… to study molecular pathways of pulmonary fibrosis. However, pathologic … in idiopathic
pulmonary fibrosis. In the bleomycin model, the fibrosis evolves over months, whereas in idiopathic …

… Idiopathic pulmonary fibrosis was the primary cause of death in 89% of patients who died,
and an apparent acute clinical deterioration preceded death in 47% of these patients. …

The natural history of idiopathic pulmonary fibrosis (IPF) has been characterized as a steady,
predictable decline in lung function over time. Recent evidence suggests that some …