Background Kawasaki disease (KD) is an acute self-limited vasculitis related to childhood
and is one of the leading causes of heart disease in children. Atypical presentations of KD
have been described in the form of thrombocytopenia, intestinal pseudo-obstruction,
torticollis, and shock. Presentation of KD with appendicitis has been rarely described. Case
presentation We present a 4-year-old girl with a negative history of recent infection and a
history of high fever (to 39.8° C) for 5 days. Blood tests, ultrasonography and …