Background Myotonic dystrophy type 1 (DM1) is associated with increased cardiac morbidity
and mortality. Therefore, assessment of cardiac involvement and risk stratification for sudden
cardiac death is crucial. Nevertheless, optimal screening-procedures are not clearly defined.
ECG, echocardiography and Holter-monitoring are useful but insufficient. Cardiovascular
magnetic resonance (CMR) can provide additional information of which myocardial fibrosis
may be relevant. The purpose of this study was to describe the prevalence of myocardial …