There have been 87 cases of superficial siderosis of the CNS reported in the world literature
and 63 cases had developed the clinical syndrome with sufficient details to be reviewed. It is
a distinct clinical syndrome characterized by sensorineural deafness (95%), cerebellar
ataxia (88%) and pyramidal signs (76%). Other features include dementia (24%), bladder
disturbance (24%), anosmia (at least 17%), aniscoria (at least 10%) and sensory signs
(13%). Less frequent features are extra-ocular motor palsies, neck or backache, bilateral …

In most patients with superficial siderosis of the CNS, the exact source of bleeding remains
unknown because of a lack of objective surgical data. The authors herein describe the case
of a 58-year-old man with superficial siderosis of the CNS. The patient also had spinal CSF
leakage due to a spinal dural defect. Repair surgery for the dural defect was performed
using posterior laminoplasty with a transdural approach without spinal fixation. During repair
surgery, the bleeding source was found to be the epidural vein around the defect. The …