Pseudomonas cepacia colonization in patients with cystic fibrosis: risk factors and clinical outcome

OC Tablan, TL Chorba, DV Schidlow, JW White… - The Journal of …, 1985 - Elsevier
… cepacia colonization or adverse outcome. 7 In our investigation, neither age nor sex was
a significant risk factor for P. cepacia colonization; however, increasing severity of underlying …

One-year outcome after severe pulmonary exacerbation in adults with cystic fibrosis

M Ellaffi, C Vinsonneau, J Coste, D Hubert… - American journal of …, 2005 - atsjournals.org
… , whereas the others were recorded as an adverse event during the follow-up of the …
two pathologic mutations in the cystic fibrosis transmembrane conductance regulator (CFTR…

Correctors (specific therapies for class II CFTR mutations) for cystic fibrosis

KW Southern, S Patel, IP Sinha… - Cochrane Database of …, 2018 - cochranelibrary.com
… that codes for that codes for the cystic fibrosis transmembrane conductance regulator (CFTR) …
outcomes in this review varied across studies. All included studies monitored the adverse

Update in cystic fibrosis 2013

M Jain, CH Goss - American journal of respiratory and critical care …, 2014 - atsjournals.org
Although cystic fibrosis (CF) continues to be the most common life-shortening genetic
disease in whites, median predicted life expectancy has reached an all-time high in the CF …

[PDF][PDF] Pregnancies and outcome in women with cystic fibrosis

A Barak, M Dulitzki, O Efrati, A Augarten, A Szeinberg… - Isr Med Assoc J, 2005 - ima.org.il
… life expectancy in cystic fibrosis and the … good outcome. In CF patients with diabetes mellitus
and gestational diabetes, both the mother and the infant had a significant adverse outcome, …

Cystic fibrosis pulmonary guidelines: chronic medications for maintenance of lung health

PA Flume, BP O'Sullivan, KA Robinson… - American journal of …, 2007 - atsjournals.org
Rationale: Cystic fibrosis is a recessive genetic disease characterized by dehydration of the …
Objectives: The Cystic Fibrosis Foundation therefore established a committee to examine …

Contraceptive safety among women with cystic fibrosis: a systematic review

MK Whiteman, T Oduyebo, LB Zapata, S Walker… - Contraception, 2016 - Elsevier
… contraception are at increased risk for adverse outcomes compared with women using other
Outcomes of interest included measures of disease severity, diabetes-related outcomes, …

[HTML][HTML] Immediate effects of lumacaftor/ivacaftor administration on lung function in patients with severe cystic fibrosis lung disease

N Popowicz, J Wood, A Tai, S Morey… - … of Cystic Fibrosis, 2017 - Elsevier
… We report immediate post-dose respiratory-related adverse events in 12 patients with severe
cystic fibrosis (CF) lung disease (median [IQR] ppFEV 1 : 34 [31–36]) prescribed LUM/IVA. …

Long term results of lung transplantation for cystic fibrosis

TM Egan, FC Detterbeck, MR Mill… - European journal of …, 2002 - academic.oup.com
… Objectives: We reviewed our experience with lung transplant for cystic fibrosis (CF) over a
10-… in the sputum of CF patients has had an adverse impact on outcome in our experience [20]. …

The outcome of pregnancies in women with cystic fibrosis—single centre experience 1998–2011

JG Thorpe‐Beeston, S Madge, K Gyi… - … Journal of Obstetrics …, 2013 - Wiley Online Library
… to address is whether pregnancy has an adverse effect on the disease course in women …
and the authors concluded that pregnancy has little adverse effect on women with stable CF, but …