Based upon data from 60 patients with congenital biliary atresia, the natural history of the
disease and its variations have been outlined. Utilizing material from 230 patients, the …

… with other congenital anatomical abnormalities. The most common is biliary atresia splenic
… cystic change within the obliterated biliary tree—termed cystic biliary atresia. At least half of …

… The timing of onset of liver injury in biliary atresia (BA) is not known, although in approximately
10% of cases, biliary pathologic condition associated with the biliary atresia splenic …

… Biliary atresia presents as an obliterative cholangiopathy with neonatal jaundice and pale
stools. The … There are other congenital anomalies such as oesophageal atresia, jejunal …

… Thus, some 10–20% of patients with BA have other congenital anomalies, including splenic
abnormalities (asplenia, polysplenia), total or partial situs inversus, mediopositioned liver, …

… the extraordinary total of 146 babies with biliary atresia, among whom they obtained a cure
… the liver before and after the relief of congenital atresia were available. Indeed, they all write …

Purpose: To evaluate prospectively the sensitivity of ultrasonography (US) in the diagnosis
of biliary atresia (BA), with surgery as the reference standard. Materials and Methods: After …

… Biliary atresia (BA) is a rare disease characterised by a biliary obstruction of unknown origin
… and narrowing or even obliteration of the biliary tree. Untreated, this condition leads to …

… About 10% (∼3% in Japanese series 1 ) of cases have other congenital abnormalities,
specifically a syndromic association which we have termed the Biliary Atresia Splenic …

… segment or all of the extrahepatic biliary tree. As the disease … With time, the intrahepatic
biliary system becomes involved. … since the first descriptions of congenital obliteration of the bile …