Rationale: Cystic fibrosis (CF) is an autosomal recessive disease characterized by abnormal
airways secretions, chronic endobronchial infection, and progressive airway obstruction. …

… of lung health for children and adults with CF. At present, the Cystic Fibrosis Foundation has
… disease, the Cystic Fibrosis Foundation established the Pulmonary Therapies Committee. …

… that pulmonary function is related to perceived health status and global quality of life in adults
suffering from cystic fibrosis… , 18–54 years) with cystic fibrosis, recruited from the Norwegian …

… Most of the morbidity and mortality in cystic fibrosis (CF) results from its pulmonary
manifestations. The CF lung is susceptible to endobronchial bacterial infection, which induces an …

… Cystic Fibrosis Foundation therefore established a committee to define the key questions
related to pulmonary … be helpful to clinicians in the treatment of individuals with cystic fibrosis. …

… in cystic fibrosis (CF) and may lead to worse health outcomes and greater health-care use.
This study evaluated associations of adherence to pulmonary medications, age, health-care …

… pulmonary disease in cystic fibrosis (CF). The molecular basis of CF lung disease including
the impact of defective cystic fibrosis … and other measures of pulmonary health are reviewed. …

… This document represents the Pulmonary Therapies Committee recommendations for the
treatment of hemoptysis and pneumothorax. The committee recognized that insufficient data …

… Short-term effects of three chest physiotherapy regimens in patients hospitalized for pulmonary
exacerbations of cystic fibrosis: a crossover randomized study. Pediatr Pulmonol 1995;19(…

… As treatment advances have improved the life expectancy of people with cystic fibrosis (CF),
understanding the impact of the disease and its treatment on everyday function and well-…