… proved to be effective in the treatment of recurrent pericarditis. Since interleukin-1 inhibition
has … that the pericarditis observed in Myhre syndrome may be autoinflammatory in nature. …

… boy of 7 years old with MYHRS who developed recurrent pericarditis with cardiac tamponade
requiring pericardiocentesis [20]. The pericardial fluid was around 200 ml and lymphocytes …

… pericardial biopsy (non-specific fibrosis) and one case of LAPS with constrictive pericardium
… claudication 22 and one case who developed recurrent pericarditis since his 7 years of age, …

… Myhre syndrome is a rare, distinctive syndrome due to specific … of Myhre syndrome who
had (i) a mildly narrow descending aorta and restrictive cardiomyopathy; (ii) recurrent pericardial …

… We confirm the severity of cardiovascular involvement in MS; the two patients with a Shone’s
complex were operated on multiple times with complications such as recurrent pericarditis. …

… case of a 7-year-old boy with Myhre syndrome who presented with life-threatening recurrent
pericarditis. Myhre syndrome is a rare genetic disorder caused by a SMAD4 mutations and …

… and pericarditis. We present five previously unreported patients with Myhre syndrome. …
Included herein is the first report of cardiac transplantation in patients with Myhre syndrome. …

… for recurrent pericarditis. Medline/Pubmed Library were screened with specific key search:
‘recurrent AND pericarditis’. … Expert opinion: An accurate diagnosis of recurrent pericarditis is …

… So far, only four SMAD4 pathogenic variants have been observed in Myhre syndrome. …
familial case of Myhre syndrome and a second adult proband with Myhre syndrome. All four …

… Pericardial disease can present as short-term or recurrent effusions, or as chronic or
progressive constrictive pericarditis that may require surgical intervention (see Management). …