… has been mirrored in research in cystic fibrosis (CF). A large … of the art of patient-reported
outcomes in CF, specifically … selection of PRO outcome measures; these outcome measures …

… 1 when the life expectancy of patients was < 1 year. … Cystic Fibrosis Foundation 6 have
contributed to the standardization of CF management. These guidelines recommend that patients …

… There is considerable variability in the clinical course of disease in cystic fibrosis (CF). …
CF patients in the United States using National Cystic Fibrosis Foundation Patient Registry (…

… Diagram of the study population of cystic fibrosis patients from the Cystic Fibrosis Foundation
Patient Registry analyzed by gender. A total of 34,693 subjects were evaluated for this …

… previously associated with a poor outcome for patients with cystic fibrosis (CF), … outcomes
of adult CF patients admitted to ICU, and to identify factors that may have influenced outcomes…

… commonly used outcome measures in CF clinical research. Other outcome measures under
… , lung injury and repair; and patient-reported outcomes. Molecular diagnostics may help …

… Other digestive outcomes in CF reviewed in this paper include meconium ileus, Clostridium
difficile infection, intussusception, acute appendicitis, small intestinal bacterial overgrowth, …

… with poor clinical outcomes. Primary clinical outcomes in the original study included pulmonary
exacerbation rates, survival and lung function, and these same outcomes are presented …

… hypothesized that patients presenting with milder cystic fibrosis, compared … cystic fibrosis
patients, and to further incorporate this “baseline risk” component for developing cystic fibrosis …

… outcomes using … outcomes and benefits, as respiratory failure remains the cause of death
in more than 95% of those diagnosed with CF, although an examination of nutritional outcomes …