Short‐term prophylaxis in hereditary angioedema due to deficiency of the C 1‐inhibitor–a long‐term survey

H Farkas, Z Zotter, D Csuka, E Szabó, Z Nébenfűhrer… - Allergy, 2012 - Wiley Online Library
Background Hereditary angioedema is a potentially life‐threatening disorder, because
edema occurring in the mucosa of the upper airways can lead to suffocation. The …

C1 esterase inhibitor concentrate in 1085 Hereditary Angioedema attacks–final results of the IMPACT 2 study

TJ Craig, AK Bewtra, SL Bahna, D Hurewitz… - Allergy, 2011 - Wiley Online Library
To cite this article: Craig TJ, Bewtra AK, Bahna SL, Hurewitz D, Schneider LC, Levy RJ, Moy
JN, Offenberger J, Jacobson KW, Yang WH, Eidelman F, Janss G, Packer FR, Rojavin MA …

Hereditary angioedema (HAE) in children and adolescents—a consensus on therapeutic strategies

V Wahn, W Aberer, W Eberl, M Faßhauer… - European journal of …, 2012 - Springer
Hereditary angioedema due to C1 inhibitor (C1 esterase inhibitor) deficiency (types I and II
HAE-C1-INH) is a rare disease that usually presents during childhood or adolescence with …

Treatment of Hereditary Angioedema.

T Caballero - Journal of Investigational Allergology & Clinical …, 2021 - europepmc.org
Hereditary angioedema due to C1-esterase inhibitor deficiency (C1-INH-HAE) is a rare
autosomal dominant disease. In the last decade, new drugs and new indications for old …

Diagnosis and screening of patients with hereditary angioedema in primary care

MP Henao, JL Kraschnewski, T Kelbel… - … and clinical risk …, 2016 - Taylor & Francis
Hereditary angioedema (HAE) is a rare autosomal dominant disease that commonly
manifests with episodes of cutaneous or submucosal angioedema and intense abdominal …

C1-inhibitor deficiency and angioedema

A Carugati, E Pappalardo, LC Zingale, M Cicardi - Molecular immunology, 2001 - Elsevier
C1-inhibitor deficiency can be inherited or acquired; both conditions lead to recurrent
angioedema that can be life threatening when the larynx is involved (hereditary …

Risk of angioedema following invasive or surgical procedures in HAE type I and II–the natural history

E Aygören‐Pürsün, I Martinez Saguer, W Kreuz… - Allergy, 2013 - Wiley Online Library
Background Hereditary angioedema (HAE), caused by deficiency in C1‐inhibitor (C1‐INH),
leads to unpredictable edema of subcutaneous tissues with potentially fatal complications …

C1‐inhibitor concentrate for individual replacement therapy in patients with severe hereditary angioedema refractory to danazol prophylaxis

W Kreuz, I Martinez‐Saguer, E Aygören‐Pürsün… - …, 2009 - Wiley Online Library
BACKGROUND: Hereditary angioedema (HAE) caused by functional deficiency of C1‐
inhibitor (C1‐INH) is a rare disease that manifests with recurrent spontaneous nonallergic …