C1-inhibitor deficiency can be inherited or acquired; both conditions lead to recurrent
angioedema that can be life threatening when the larynx is involved (hereditary …

Background Acquired angioedema due to C1-inhibitor deficiency (C1-INH-AAE) is a rare
disease with no prevalence data or approved therapies. Objective To report data on patients …

Acquired deficiency of C1 inhibitor (C1-INH) with angioedema symptoms (acquired
angioedema, AAE) is characterized by local increase in vascular permeability (agioedema) …

BACKGROUND: C1 Inhibitor (C1-Inh) deficiency causes angioedema and can be hereditary
(HAE), caused by mutations in the C1-Inh gene (C1NH), or acquired (AAE). Patients with …

Hereditary angioedema (HAE) is an autosomal dominant inheritable disorder that is caused
by a heterozygous deficiency in the plasma protein, C1-inhibitor (C1-INH). The role of C1 …

Angioedema due to acquired C1-inhibitor (C1-INH) deficiency (also referred to as “acquired
angioedema”) is a rare, life-threatening disease with poorly defined etiology, therapy, and …

Angioedema due to an acquired deficiency in the inhibitor of the first component of human
complement (CI-INH) is a rare syndrome that is usually identified as acquired angioedema …

C1 inhibitor (C1-Inh) is a protease inhibitor of the serpin family. It interacts and forms
complexes with several serine proteases although not all these interactions were proved to …

Hereditary angioedema due to C1-inhibitor deficiency (HAE-C1-INH) is a rare, autosomal-
dominant disease. HAE-C1-INH is characterized by recurrent attacks of marked, diffuse …

BACKGROUND: Hereditary angioedema (HAE) is caused by heterozygous defects in the C1
inhibitor (C1-INH) gene (SERPING1/C1NH). In patients' plasma C1-INH levels range …