Background and purpose Cardiac involvement is observed in about 80% of subjects with
myotonic dystrophy type 1 (DM1) and is mainly characterized by cardiac conduction and/or …

Background Patients with myotonic dystrophy type 1 (DM1) have a three-fold higher risk of
sudden cardiac death (SCD) than age-matched healthy controls. Despite numerous …

Background Frequency and severity of cardiac involvement in DM2 are still controversial.
The aims of our study were to determine the frequency and progression of cardiac and …

Abstract Myotonic dystrophy type 2 (DM2) is a slowly progressive, autosomal-dominant
disease. This is a multisystemic disorder that affects the heart, which is one of the main …

Aims To describe the incidence and identify predictors of sudden death (SD), major
conduction defects and sustained ventricular tachyarrhythmias (VTA) in myotonic dystrophy …

Background Cardiac involvement represents a major cause of morbidity and mortality in
patients with myotonic dystrophy type 1 (DM1) and prevention of sudden cardiac death …

The aim of this study was to analyze survival, causes of death and cardiologic predictors of
sudden death in a large cohort of patients with myotonic dystrophy type 1 (DM1). The study …

Arrhythmias in Myotonic Dystrophy Patients Background Myotonic dystrophy (MD) is the
most common muscular dystrophy in adults and is associated with sudden death. Reported …

BACKGROUND: Myotonic dystrophy type 1 (DM1) is a neurological disorder with known
cardiac involvement, including conduction disturbances, arrhythmias, and ventricular …

Objective Myotonic dystrophy type 1 (DM1) is the most frequent muscular dystrophy in
adults. DM1 is a multisystem disorder also affecting the heart with an increased incidence of …